Rizzuto Antonia, Di Saverio Salomone
Department of Medical and Surgical Sciences, University Magna Græcia of Catanzaro, Italy.
Maggiore Hospital Regional Emergency Surgery and Trauma Center, Bologna Local Health District, Bologna, Italy.
Int J Surg Case Rep. 2018;43:36-40. doi: 10.1016/j.ijscr.2018.01.017. Epub 2018 Feb 9.
Wandering spleen and accessory spleen are uncommon entity occurring during embryonic development. Wandering spleen results in an excessive mobility and migration of the spleen from its normal position in the left hypochondrium while accessory spleen is characterized by ectopic splenic masses or tissue disjointed from the main body of spleen. Due to the nonspecific and multiple symptoms the clinical diagnosis of both conditions is uncertain even with imaging techniques, such as CT and MRI. The coexistence of both diseases (wandering spleen ad accessory spleen) is uncommon.
A 17-year old European female with a history of minor beta thalassemia and recurrent attacks of abdominal pain. Pre- operative management consisted of routine laboratory tests, ultrasound, CT scan. An ectopic spleen along with an accessory spleen were diagnosed. After a multidisciplinary board a laparoscopic splenectomy was performed. Post-operative recovery was uneventful, and the patient was discharged on the 6th post-operative day with the indication to continue the therapy with low molecular weight heparin (LMWH) for 30 days CONCLUSIONS: This case represents a simultaneous condition of wandering splenomegaly along with an ectopic wandering spleen. The coexistence of these two rare conditions is peculiar such as the age of the patient, as literature reports such diseases to affect children or more commonly people in the range of 20-40 years of age. Laparoscopic treatment for this particular condition is also unusual.
游走脾和副脾是胚胎发育过程中出现的罕见情况。游走脾导致脾脏从左季肋区的正常位置过度移动和迁移,而副脾的特征是异位脾块或与脾脏主体分离的组织。由于症状不具特异性且多样,即使采用CT和MRI等成像技术,这两种情况的临床诊断也不明确。这两种疾病(游走脾和副脾)并存并不常见。
一名17岁的欧洲女性,有轻度β地中海贫血病史且反复腹痛发作。术前管理包括常规实验室检查、超声、CT扫描。诊断出一个异位脾和一个副脾。经过多学科会诊后,进行了腹腔镜脾切除术。术后恢复顺利,患者在术后第6天出院,并被指示继续使用低分子量肝素(LMWH)治疗30天。结论:本病例代表了游走性脾肿大与异位游走脾同时存在的情况。这两种罕见情况的并存很特殊,患者的年龄也是如此,因为文献报道此类疾病影响儿童或更常见的是20至40岁年龄段的人。针对这种特殊情况的腹腔镜治疗也不常见。