Akhavan Setareh, Agah Jila, Nili Fatemeh
Department of Gynecology Oncology, Vali-Asr Hospital, Tehran University of Medical Sciences, Tehran, Iran.
Department of Obstetrics and Gynecology Oncology, Sabzevar University of Medical Sciences, Sabzevar, Iran.
J Obstet Gynaecol Res. 2018 May;44(5):978-982. doi: 10.1111/jog.13609. Epub 2018 Feb 27.
A G2L2 33-year-old woman presented to our clinic with large verrucous warty masses in labia major, perinea and the end portion of her spine measuring about 15 × 7, 9 × 7 and 8 × 8 cm, which had been enlarged following puberty and pregnancy. Her right upper and left lower limbs had gross congenital lymphedema. The masses were removed by superficial partial vulvectomy with a qualified margin and repaired without skin graft. Pathology report showed lymphangioma circumscriptum. Several months of follow up revealed normal healing and no recurrence. In conclusion, congenital vulvar lymphangioma, which is a rare disorder, can be highly triggered by hormonal-stimulating situations like puberty and pregnancy. Thus, it is better to visit the affected cases in a timely manner in order to excise these lesions before massive enlargement. In our experience, a superficial partial vulvectomy without skin graft can be a sufficient procedure. Obviously, an appropriate approach during and after surgery would be very important for obtaining a desirable healing.
一名33岁的G2L2女性因大阴唇、会阴和脊柱末端出现大约15×7厘米、9×7厘米和8×8厘米的巨大疣状肿块前来我院就诊，这些肿块在青春期和怀孕后增大。她的右上和左下肢有明显的先天性淋巴水肿。通过浅部部分外阴切除术切除肿块，切缘合格，未植皮进行修复。病理报告显示为局限性淋巴管瘤。数月随访显示愈合正常，无复发。总之，先天性外阴淋巴管瘤是一种罕见疾病，可由青春期和怀孕等激素刺激情况高度诱发。因此，最好及时诊治这些病例，以便在肿块大量增大之前切除这些病变。根据我们的经验，不植皮的浅部部分外阴切除术可能是一种充分的手术方法。显然，手术期间和术后采取适当的方法对于获得理想的愈合非常重要。
