Vatopoulou Anastasia, Anagnostopoulos Antonios, Sujeewa Fernando
First Department of Obstetrics and Gynecology, Medical School, Aristotle University Thessaloniki, Papageorgiou Hospital, Thessaloniki, Greece.
Department of Obstetrics and Gynecology, Wrexham Maelor Hospital, Wrexham, UK.
J Obstet Gynaecol Res. 2019 Oct;45(10):2137-2138. doi: 10.1111/jog.14086. Epub 2019 Jul 30.
Lymphangioma circumscriptum is a rare benign disorder of unknown etiology affecting lymph vessels in the deep dermal and subcutaneous layers. The commonest sites of presentation are the axilla, shoulders, groins, tongue and oral cavity. Lymphangioma circumscriptum of the vulva is very rare can be either congenital or secondary to lymphadenectomy or pelvic radiation in patients with genital cancer, genital tuberculosis, Crohn's disease, cellulitis, morbid obesity and immobilization. We report the case of congenital lymphangioma circumscriptum of the vulva in an adolescent with congenital lymphedema of the leg.
局限性淋巴管瘤是一种病因不明的罕见良性疾病，影响真皮深层和皮下层的淋巴管。最常见的发病部位是腋窝、肩部、腹股沟、舌头和口腔。外阴局限性淋巴管瘤非常罕见，可为先天性，也可继发于患有生殖系统癌症、生殖系统结核、克罗恩病、蜂窝织炎、病态肥胖症和长期卧床的患者进行的淋巴结切除术或盆腔放疗。我们报告了一名患有先天性腿部淋巴水肿的青少年外阴先天性局限性淋巴管瘤的病例。
