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肾盂成形术后尿崩症的缓解:一例病例报告及文献复习

Resolution of Diabetes Insipidus After Pyeloplasty: A Case Report and Review of the Literature.

作者信息

Carpenter Christina P, Rawson Ashley, Hains David S, Giel Dana W

机构信息

Division of Pediatric Urology, Le Bonheur Children's Hospital, Memphis, TN; Department of Urology, The University of Tennessee Health Science Center, Memphis, TN.

Division of Nephrology, Riley Hospital for Children, Indianapolis, IN; Department of Pediatrics, Indiana University School of Medicine, Indianapolis, IN.

出版信息

Urology. 2018 May;115:168-170. doi: 10.1016/j.urology.2018.02.017. Epub 2018 Feb 28.

DOI:10.1016/j.urology.2018.02.017
PMID:29499256
Abstract

Nephrogenic diabetes insipidus (NDI), a rare cause of polyuria and polydipsia in children, is usually managed with medications and careful monitoring of water intake. We present a child who was incidentally found to have right hydronephrosis secondary to ureteropelvic junction obstruction, and was subsequently also diagnosed with NDI. After being medically managed, he underwent open right pyeloplasty. His polydipsia abated within 1 month of surgery, and he has done well off of medications since that time. NDI resolution after correction of obstructive uropathy in adults has been reported, but this represents a novel case in pediatrics.

摘要

肾性尿崩症(NDI)是儿童多尿和烦渴的罕见病因,通常通过药物治疗并仔细监测水摄入量来处理。我们报告一名儿童,他偶然被发现因肾盂输尿管连接处梗阻继发右侧肾积水,随后也被诊断为肾性尿崩症。在接受药物治疗后,他接受了开放性右侧肾盂成形术。术后1个月内他的烦渴症状减轻,自那时起停药后情况良好。成人梗阻性肾病纠正后肾性尿崩症缓解已有报道,但这在儿科是一个新病例。

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引用本文的文献

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Asymptomatic obstructive hydronephrosis associated with diabetes insipidus: a case report and review.与尿崩症相关的无症状性梗阻性肾积水:一例病例报告及文献复习
Transl Pediatr. 2021 Jun;10(6):1721-1727. doi: 10.21037/tp-20-476.
2
Congenital nephrogenic diabetes insipidus accompanied with central nephrogenic diabetes secondary to pituitary surgery -a case report.先天性肾性尿崩症伴垂体手术后中枢性肾性尿崩症 - 病例报告。
BMC Endocr Disord. 2021 Apr 21;21(1):78. doi: 10.1186/s12902-021-00749-y.