Dias-Polak David, Indelman Margarita, Bergman Reuven, Avitan-Hersh Emily
Department of Dermatology Rambam Health Care Campus HaAliya HaShniya St 8, Haifa POB 9602 Haifa 31096 Israel.
Laboratory of Molecular Dermatology The Bruce Rappaport Faculty of Medicine, Technion Rambam Health Care Campus HaAliya HaShniya St 8, Haifa POB 9602 Haifa 31096 Israel.
Clin Case Rep. 2018 Jan 25;6(3):476-478. doi: 10.1002/ccr3.1329. eCollection 2018 Mar.
Skin biopsy may be helpful in the diagnosis of H syndrome. A triad of dermal fibrosis, lymphocytic aggregates, and numerous CD68+, CD163+, S100-positive, and CD1a-negative dermal histiocytes is characteristic.
皮肤活检可能有助于H综合征的诊断。真皮纤维化、淋巴细胞聚集以及大量CD68+、CD163+、S100阳性和CD1a阴性的真皮组织细胞构成的三联征具有特征性。