Beliaeva E V, Lapshina L V, Shaposhnikova E V, Molgachev A A
Maternity Home #4, Krasnoyarsk, Russia.
Maternity Home #4, Krasnoyarsk, Russia; Voino-Yasenetsky Krasnoyarsk State Medical University, Krasnoyarsk, Russia.
Zh Nevrol Psikhiatr Im S S Korsakova. 2018;118(2):85-89. doi: 10.17116/jnevro20181182185-89.
Dandy-Walker malformation is a rare disease of the central nervous system pathology (congenital malformations of the fossa cranii posterior). The key features of this syndrome are an enlargement of the fourth ventricle; complete absence of the cerebellar vermis, the posterior midline area of cerebellar cortex responsible for coordination of the axial musculature; and cyst formation near the internal base of the skull. Pregnant patients with Dandy-Walker malformation are at high risk and are managed by multidisciplinary teams including neurologists and obstetricians. We present a case report of full-term pregnancy and uncomplicated delivery in a women with Dandy-Walker malformation.
丹迪-沃克畸形是一种罕见的中枢神经系统病理学疾病（颅后窝先天性畸形）。该综合征的关键特征是第四脑室扩大；小脑蚓部完全缺失，小脑蚓部是小脑皮质负责轴性肌肉协调的后中线区域；以及在颅底内侧附近形成囊肿。患有丹迪-沃克畸形的孕妇风险很高，由包括神经科医生和产科医生在内的多学科团队进行管理。我们报告一例患有丹迪-沃克畸形的女性足月妊娠且分娩顺利的病例。
