Franken E A, Smith W L, Frey E E, Sato Y, Anuras S
Department of Radiology, University of Iowa College of Medicine, Iowa City.
Crit Rev Diagn Imaging. 1987;27(3):203-36.
Diseases affecting intestinal motility in the pediatric age group are reviewed as to pathophysiology, clinical manifestations, and imaging investigation. Acute disease includes classical paralytic ileus (which has unique causes and manifestations in the infant) and acute regional bowel paralysis. Perinatal motility disorders consist of a group of related clinical syndromes which have in common functional intestinal obstruction. Chronic motility disorders are divided into those diseases in which the principal abnormality is in the bowel or those entities where the gut is affected as part of a generalized disease. Regional muscle disease includes Hirschsprung's disease and allied disorders. Some recognized causes of chronic functional obstruction of bowel include megacystis-microcolon-intestinal hypoperistalsis syndrome, rare enzymatic disorders, several discrete forms of chronic intestinal pseudoobstruction, as well as some less well-defined entities. Clinical and pathologic nature and methods of imaging investigation of these entities are considered.
本文对影响儿童肠道动力的疾病进行了综述,内容涵盖病理生理学、临床表现及影像学检查。急性疾病包括典型的麻痹性肠梗阻(在婴儿中有独特病因及表现)和急性节段性肠麻痹。围产期动力障碍由一组相关临床综合征组成,其共同特征为功能性肠梗阻。慢性动力障碍分为主要肠道异常的疾病以及肠道作为全身性疾病一部分而受影响的疾病。节段性肌肉疾病包括先天性巨结肠及其相关疾病。一些公认的慢性肠道功能性梗阻病因包括巨膀胱-微小结肠-肠蠕动减弱综合征、罕见的酶缺乏症、几种不同形式的慢性假性肠梗阻,以及一些定义不太明确的疾病。本文还探讨了这些疾病的临床及病理性质以及影像学检查方法。