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与精神障碍及母乳喂养相关的成人坏血病

Adult scurvy associated with psychiatric disorders and breast feeding.

作者信息

Urueña-Palacio Stefania, Ferreyro Bruno L, Fernández-Otero Lucas G, Calo Pablo D

机构信息

Department of Internal Medicine, Hospital Italiano de Buenos Aires, Autonomous City of Buenos Aires, Argentina.

Department of Internal Medicine, Hospital Italiano de San Justo Agustín Rocca, San Justo, Buenos Aires, Argentina.

出版信息

BMJ Case Rep. 2018 Mar 30;2018:bcr-2017-223686. doi: 10.1136/bcr-2017-223686.

DOI:10.1136/bcr-2017-223686
PMID:29602889
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC5884256/
Abstract

Scurvy is a nutritional disease caused by ascorbic acid deficiency and is potentially fatal. It was originally described in the 18th century by James Lind and associated with long sea voyages and insufficient citrus consumption. Its prevalence has declined markedly over the years but has still been described sporadically in certain countries. A 22-year-old woman with an anxiety disorder and anorexia nervosa, recent pregnancy and ongoing breast feeding, presented with a 10-day history of spontaneous haematomas in the lower limbs, gingivorrhagia and fatigue. The examination was remarkable for signs of minor bleeding without haemodynamic compromise, gonalgia and pale skin. Work-up studies revealed the presence of anaemia. Direct anamnesis identified a diet based solely of tea and carbohydrates due to distorted body image. With the working diagnosis of scurvy, nutritional support and oral vitamin C supplementation was initiated. Her symptoms and anaemia resolved in 30 days and the diagnosis was confirmed biochemically.

摘要

坏血病是一种由抗坏血酸缺乏引起的营养性疾病,有潜在致命风险。它最初在18世纪由詹姆斯·林德描述,与长期海上航行和柑橘类水果摄入不足有关。多年来其发病率已显著下降,但在某些国家仍有散发病例报道。一名22岁患有焦虑症和神经性厌食症、近期怀孕且正在哺乳的女性,出现下肢自发性血肿、牙龈出血和疲劳10天的症状。检查发现有轻微出血迹象但无血流动力学障碍、关节痛和皮肤苍白。检查研究显示存在贫血。直接问诊发现由于身体形象扭曲,其饮食仅为茶和碳水化合物。根据坏血病的初步诊断,开始给予营养支持和口服维生素C补充剂。她的症状和贫血在30天内得到缓解,生化检查确诊了诊断。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/676d/5884256/559da7cc1c0b/bcr-2017-223686f03.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/676d/5884256/eb9ddd159da9/bcr-2017-223686f01.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/676d/5884256/152d9a464bdc/bcr-2017-223686f02.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/676d/5884256/559da7cc1c0b/bcr-2017-223686f03.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/676d/5884256/eb9ddd159da9/bcr-2017-223686f01.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/676d/5884256/152d9a464bdc/bcr-2017-223686f02.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/676d/5884256/559da7cc1c0b/bcr-2017-223686f03.jpg

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No longer a historical ailment: two cases of childhood scurvy with recommendations for bone health providers.不再是历史遗留疾病:两例儿童坏血病病例及对骨骼健康提供者的建议。

本文引用的文献

1
A disease of the present: scurvy in "well-nourished" patients.当下的一种疾病:“营养良好”患者中的坏血病。
J Am Acad Dermatol. 2013 Nov;69(5):e246-e247. doi: 10.1016/j.jaad.2013.04.051.
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Scurvy in a man with schizophrenia.一名患有精神分裂症的男子患坏血病。
CMAJ. 2011 Aug 9;183(11):E760. doi: 10.1503/cmaj.080505. Epub 2011 May 9.
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Stranded in San Francisco.被困在旧金山。
Osteoporos Int. 2020 May;31(5):1001-1005. doi: 10.1007/s00198-019-05264-4. Epub 2020 Jan 4.
Lancet. 2008 Sep 13;372(9642):1008. doi: 10.1016/S0140-6736(08)61410-5.
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Worldwide prevalence of anaemia, WHO Vitamin and Mineral Nutrition Information System, 1993-2005.全球贫血患病率,世界卫生组织维生素和矿物质营养信息系统,1993 - 2005年
Public Health Nutr. 2009 Apr;12(4):444-54. doi: 10.1017/S1368980008002401. Epub 2008 May 23.
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Scurvy is still present in developed countries.坏血病在发达国家仍然存在。
J Gen Intern Med. 2008 Aug;23(8):1281-4. doi: 10.1007/s11606-008-0577-1. Epub 2008 May 6.
6
Old world meets modern: a case report of scurvy.旧世界与现代相遇:坏血病病例报告
Nutr Clin Pract. 2007 Aug;22(4):445-8. doi: 10.1177/0115426507022004445.
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Adult scurvy.成人坏血病
J Am Acad Dermatol. 1999 Dec;41(6):895-906; quiz 907-10. doi: 10.1016/s0190-9622(99)70244-6.
8
New concepts in the biology and biochemistry of ascorbic acid.抗坏血酸生物学与生物化学的新概念
N Engl J Med. 1986 Apr 3;314(14):892-902. doi: 10.1056/NEJM198604033141407.