Cardama J E, Gatti J C, Olivares L M, Pizzariello G E, Lebek A P, Romorini A
División de Medicina, Hospital F.J. Muñiz.
Med Cutan Ibero Lat Am. 1987;15(4):265-73.
Two females patients with CREST syndrome associated with cardiac involvement are reported. One of them has pericardial effusion just shown by echocardiography with patterns of cardiomyopathy of ventricular cavities, the latter as primary myocardial involvement, in the absence of pulmonary or systemic hypertension. The second patient has chronic cor pulmonale secondary to pulmonary hypertension verified by electrocardiography and echocardiography. It is emphasized the utility of the echocardiography and the importance of those anomalies that can lead to the patient's death, transforming the CREST towards a syndrome with potentially but late, severe systemic involvement.
报道了两名患有伴有心脏受累的CREST综合征的女性患者。其中一名患者仅通过超声心动图显示有心包积液，伴有心室腔心肌病模式，后者为原发性心肌受累，无肺动脉或系统性高血压。第二名患者经心电图和超声心动图证实患有继发于肺动脉高压的慢性肺源性心脏病。强调了超声心动图的实用性以及那些可能导致患者死亡的异常情况的重要性，这些异常情况使CREST综合征转变为一种潜在但晚期有严重全身受累的综合征。
