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伪装成复发性室间隔缺损的先天性主动脉瓣周隧道

Congenital aortic paravalvular tunnel masquerading as a recurrent ventricular septal defect.

作者信息

Bakas Anna M, Vardas Panos N, Farrell Anne G, Rodefeld Mark D

机构信息

Divisions of Cardiothoracic Surgery, Riley Hospital for Children at IU Health, Indiana University School of Medicine, Indianapolis, Indiana.

Divisions of Cardiology, Riley Hospital for Children at IU Health, Indiana University School of Medicine, Indianapolis, Indiana.

出版信息

J Card Surg. 2018 May;33(5):289-291. doi: 10.1111/jocs.13573. Epub 2018 Apr 11.

DOI:10.1111/jocs.13573
PMID:29638016
Abstract

A 4-year-old female underwent surgical repair of an unusual variation of an aorto-left ventricular tunnel (ALVT). Serial echocardiograms had demonstrated previous spontaneous closure of a perimembranous ventricular septal defect (VSD). The patient presented with concern for residual VSD which was later demonstrated to be an eccentric jet through an ALVT. This case emphasizes early and accurate diagnosis for ALVTs and how they can be misdiagnosed as VSDs.

摘要

一名4岁女性接受了主动脉-左心室隧道(ALVT)异常变异的手术修复。系列超声心动图显示之前膜周部室间隔缺损(VSD)已自然闭合。该患者因担心存在残余VSD前来就诊,后来发现是通过ALVT的偏心血流束。本病例强调了ALVT的早期准确诊断以及它们如何被误诊为VSD。

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Congenital aortic paravalvular tunnel masquerading as a recurrent ventricular septal defect.伪装成复发性室间隔缺损的先天性主动脉瓣周隧道
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Aortico-left ventricular tunnel with ventricular septal defect: two-dimensional/Doppler echocardiographic diagnosis.主动脉-左心室隧道合并室间隔缺损:二维/多普勒超声心动图诊断
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引用本文的文献

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Aorto-Left Ventricular Tunnel: The First Systematic Review of An Uncommon Entity (177 Worldwide Cases from 1965 to 2024).主动脉-左心室隧道:对一种罕见病症的首次系统综述(1965年至2024年全球177例病例)
Rev Cardiovasc Med. 2025 Feb 20;26(2):26005. doi: 10.31083/RCM26005. eCollection 2025 Feb.