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主动脉-左心室隧道合并室间隔缺损:二维/多普勒超声心动图诊断

Aortico-left ventricular tunnel with ventricular septal defect: two-dimensional/Doppler echocardiographic diagnosis.

作者信息

Bash S E, Huhta J C, Nihill M R, Vargo T A, Hallman G L

出版信息

J Am Coll Cardiol. 1985 Mar;5(3):757-60. doi: 10.1016/s0735-1097(85)80408-3.

DOI:10.1016/s0735-1097(85)80408-3
PMID:3973274
Abstract

Aortico-left ventricular tunnel is a rare congenital anomaly that presents as aortic regurgitation and congestive heart failure in childhood. Its association with a ventricular septal defect is even more rare. Because of the distortion of the normal anatomy around the aortic valve and the rarity of this combination of defects, the diagnosis of aortico-left ventricular tunnel with ventricular septal defect may be difficult. The two-dimensional and Doppler echocardiographic findings of aortico-left ventricular tunnel are described.

摘要

主动脉-左心室通道是一种罕见的先天性异常,在儿童期表现为主动脉瓣反流和充血性心力衰竭。它与室间隔缺损同时存在的情况更为罕见。由于主动脉瓣周围正常解剖结构的扭曲以及这种缺陷组合的罕见性,合并室间隔缺损的主动脉-左心室通道的诊断可能具有挑战性。本文描述了主动脉-左心室通道的二维及多普勒超声心动图表现。

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J Am Coll Cardiol. 1985 Mar;5(3):757-60. doi: 10.1016/s0735-1097(85)80408-3.
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引用本文的文献

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Aorto-Left Ventricular Tunnel: The First Systematic Review of An Uncommon Entity (177 Worldwide Cases from 1965 to 2024).主动脉-左心室隧道:对一种罕见病症的首次系统综述(1965年至2024年全球177例病例)
Rev Cardiovasc Med. 2025 Feb 20;26(2):26005. doi: 10.31083/RCM26005. eCollection 2025 Feb.
2
Aorto-Right Ventricular Tunnel in Transposition of the Great Arteries.大动脉转位中的主动脉-右心室通道
Front Pediatr. 2018 Feb 21;6:30. doi: 10.3389/fped.2018.00030. eCollection 2018.
3
Clinical value of diagnosing aortico-left ventricular tunnel by echocardiography.
超声心动图诊断主动脉-左心室隧道的临床价值。
Exp Ther Med. 2016 Nov;12(5):3315-3319. doi: 10.3892/etm.2016.3747. Epub 2016 Sep 23.
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Aorto-ventricular tunnel.主动脉心室通道
Orphanet J Rare Dis. 2007 Oct 8;2:41. doi: 10.1186/1750-1172-2-41.
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Role of transesophageal echocardiography in the management of aortic-left ventricular tunnel.经食管超声心动图在主动脉-左心室隧道管理中的作用
Pediatr Cardiol. 1995 May-Jun;16(3):137-40. doi: 10.1007/BF00801913.
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Echocardiographic-anatomical correlations in aorto-left ventricular tunnel.主动脉-左心室隧道的超声心动图与解剖学相关性
Br Heart J. 1995 Oct;74(4):443-8. doi: 10.1136/hrt.74.4.443.
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Rupture of a sinus of Valsalva aneurysm in a neonate.新生儿主动脉窦瘤破裂
Eur J Pediatr. 1990 Jun;149(9):603-4. doi: 10.1007/BF02034741.
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Aortico-left ventricular tunnel associated with critical aortic stenosis in the newborn.新生儿主动脉左心室通道合并严重主动脉瓣狭窄
Pediatr Cardiol. 1991 Oct;12(4):237-40. doi: 10.1007/BF02310574.