García-Ortega D Y, Clara-Altamirano M A, Montaño-Gómez D, Martínez-Said H, Caro-Sánchez C H S, Cuéllar-Hubbe M
Departamento de Piel y Partes Blandas del Instituto Nacional de Cancerología. Avenida San Fernando 22, Belisario Domínguez Secc 16, 14080. Ciudad de México. México.
Ortopedia Oncológica, Instituto Nacional de Rehabilitación, Calz México-Xochimilco 289, Arenal de Guadalupe, 14389. Ciudad de México. México.
Acta Ortop Mex. 2017 Nov-Dec;31(6):308-311.
Pigmented villonodular synovitis (PVNS) is a rare clinical entity with higher incidence in women (3:1) and an age of presentation between 20 and 40 years. The hip is a rare site of appearance, being involved in only 15% of all cases.
47-year-old male with 10 years of evolution characterized by a limited range of motion, pain associated with an increase in volume and shortening of the pelvic limb. Imaging studies showed destruction of the hip joint and extension to the pelvis. The histopathology report described pigmented villonodular synovitis. His final treatment was left hemipelvectomy.
The presentation of the diffuse pigmented villonodular synovitis of the hip has a lower incidence and a locally aggressive behavior. It is necessary to consider differential diagnoses that include malignant neoplasms. The standard treatment is surgical.
色素沉着绒毛结节性滑膜炎（PVNS）是一种罕见的临床病症，女性发病率较高（3:1），发病年龄在20至40岁之间。髋关节是其罕见的发病部位，仅占所有病例的15%。
一名47岁男性，病程10年，表现为活动范围受限、疼痛，伴有骨盆肢体体积增大和缩短。影像学检查显示髋关节破坏并累及骨盆。组织病理学报告描述为色素沉着绒毛结节性滑膜炎。其最终治疗为左侧半骨盆切除术。
髋关节弥漫性色素沉着绒毛结节性滑膜炎的发病率较低且具有局部侵袭性。有必要考虑包括恶性肿瘤在内的鉴别诊断。标准治疗方法是手术治疗。
