Hématologie, Hôpital de La Source, CHR Orléans, Orléans, France.
Médecine Interne, Hôpital Haut Lévêque, Pessac, France.
Eur J Haematol. 2018 Jul;101(1):48-56. doi: 10.1111/ejh.13078. Epub 2018 May 17.
To describe the characteristics of patients suffering from secondary immunodeficiencies (SID) associated with hematological malignancies (HM), who started immunoglobulin replacement therapy (IgRT), physicians' expectations regarding IgRT, and IgRT modalities.
Non-interventional, prospective French cross-sectional study.
The analysis included 231 patients (66 ± 12 years old) suffering from multiple myeloma (MM) (N = 64), chronic lymphoid leukemia (CLL) (N = 84), aggressive non-Hodgkin B-cell lymphoma (aNHL) (N = 32), indolent NHL (N = 39), acute leukemia (N = 6), and Hodgkin disease (N = 6). Of the HM, 47% were currently treated, 42% were relapsing or refractory, 23% of patients had received an autologous hematopoietic stem-cell transplant, and 1% had received an allograft. Serum immunoglobulin trough levels in 195 individuals were less than 5 g/L in 68.7% of cases. Most patients had a history of recurrent infections. Immunoglobulin dose was about 400 mg/kg/mo. Half of patients started with subcutaneous infusion. When starting IgRT, physicians mainly expected to prevent severe and moderate infections. They also anticipated improvement in quality of life and survival which is beyond evidence-based medicine.
NHL is a frequent condition motivating IgRT besides well-recognized indications. Physicians mainly based the decision of starting IgRT on hypogammaglobulinemia and recurrence of infections but, irrespective of current recommendations, were also prepared to start IgRT prophylactically even in the absence of a history of infections.
描述与血液恶性肿瘤(HM)相关的继发性免疫缺陷(SID)患者的特征,这些患者开始接受免疫球蛋白替代治疗(IgRT),描述医生对 IgRT 的期望以及 IgRT 方式。
非干预性、前瞻性法国横断面研究。
分析纳入了 231 名患者(66±12 岁),患有多发性骨髓瘤(MM)(N=64)、慢性淋巴细胞白血病(CLL)(N=84)、侵袭性非霍奇金 B 细胞淋巴瘤(aNHL)(N=32)、惰性 NHL(N=39)、急性白血病(N=6)和霍奇金病(N=6)。HM 中,47%正在接受治疗,42%处于复发或难治阶段,23%的患者接受了自体造血干细胞移植,1%接受了同种异体移植。195 名个体的血清免疫球蛋白谷底水平,68.7%的病例低于 5g/L。大多数患者有反复感染的病史。免疫球蛋白剂量约为 400mg/kg/mo。一半的患者开始接受皮下输注。开始 IgRT 时,医生主要期望预防严重和中度感染。他们还期望改善生活质量和生存,这超出了循证医学的范围。
除了公认的适应证外,NHL 也是激发 IgRT 的常见病症。医生主要根据低丙种球蛋白血症和感染复发决定开始 IgRT,但无论目前的建议如何,即使没有感染史,他们也准备预防性地开始 IgRT。