Savader S J, Savader B L, Otero R R
Department of Radiology, University of South Florida College of Medicine, Tampa 33612.
Acta Radiol. 1988 Jan-Feb;29(1):109-14.
Primary (congenital) intraosseous arteriovenous malformations are rare, accounting for less than one per cent of all primary intraosseous lesions. They are quite variable in their gross and microscopic presentation, yet all can be traced to anomalous development of the primitive vascular system. They may be totally asymptomatic, cosmetically disfiguring, painful, or on rare occasions, cause high-output cardiac failure. Surgical treatment is often unrewarding with recurrence not uncommon. Intra-arterial embolization has shown promising results. We present three cases of primary intraosseous arteriovenous malformations which on initial work-up mimicked malignant disease. Arteriography proved diagnostic in all three cases.
原发性(先天性)骨内动静脉畸形很罕见,占所有原发性骨内病变的比例不到1%。其大体和显微镜下表现差异很大,但均可追溯到原始血管系统的异常发育。它们可能完全无症状,也可能导致外貌毁损、疼痛,或在极少数情况下引起高输出量心力衰竭。手术治疗往往效果不佳,复发并不少见。动脉内栓塞已显示出有前景的结果。我们报告3例原发性骨内动静脉畸形病例,其在初始检查时疑似恶性疾病。血管造影在所有3例中均确诊。