Arunakumar Priyadarshini, Ayyappan Anoop, Sasikumar Deepa, Krishnamoorthy K M
Department of Cardiology, Sree Chitra Tirunal Institute for Medical Sciences and Technology, Trivandrum, India.
Department of Radiology, Sree Chitra Tirunal Institute for Medical Sciences and Technology, SCTIMST, Thiruvananthapuram, India.
Echocardiography. 2018 May;35(5):733-734. doi: 10.1111/echo.13880. Epub 2018 Apr 12.
A 12-year-old child presented with recurrent respiratory infections and was diagnosed with Scimitar syndrome. Drainage of IVC and course of aberrant arterial supply from aorta were not clear by echocardiogram, and hence, additional imaging was planned. CT unraveled the presence of a rare combination of anomalous pulmonary venous connection (APVC) to IVC, with near-atresia/severe stenosis of IVC, superior to the drainage of scimitar vein. There was a prominent azygos vein with preferential contrast opacification on lower limb injection.
一名12岁儿童因反复呼吸道感染就诊，被诊断为弯刀综合征。超声心动图显示下腔静脉引流及主动脉异常动脉供应情况不明，因此计划进行进一步影像学检查。CT检查发现存在一种罕见的异常组合，即肺静脉异常连接至下腔静脉，同时下腔静脉近闭锁/严重狭窄，位于弯刀状静脉引流上方。存在一条明显的奇静脉，在下肢注射造影剂时造影剂优先显影。
