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巨大纵隔脂肪肉瘤:一种罕见但独特的临床实体。

Giant Mediastinal Liposarcoma: A Rare Yet Distinct Clinical Entity.

机构信息

Division of General Thoracic Surgery, Michael E. DeBakey Department of Surgery, Baylor College of Medicine, Houston, Texas.

Department of Pathology and Immunology, Baylor College of Medicine, Houston, Texas.

出版信息

Ann Thorac Surg. 2018 Sep;106(3):e117-e119. doi: 10.1016/j.athoracsur.2018.03.018. Epub 2018 Apr 12.

DOI:10.1016/j.athoracsur.2018.03.018
PMID:29654722
Abstract

Mediastinal liposarcomas are rare tumors that occasionally present as unusually large and rapidly growing mediastinal masses resulting in compressive symptoms. We present a case of a 48-year-old woman undergoing resection of a mediastinal liposarcoma of massive proportion and propose that "giant mediastinal liposarcomas" be identified as a distinct clinical entity.

摘要

纵隔脂肪肉瘤是一种罕见的肿瘤,偶尔会表现为异常大且快速生长的纵隔肿块,导致压迫症状。我们报告了一例 48 岁女性接受巨大纵隔脂肪肉瘤切除术的病例,并提出“巨大纵隔脂肪肉瘤”应被视为一种独特的临床实体。

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Giant Mediastinal Liposarcoma: A Rare Yet Distinct Clinical Entity.巨大纵隔脂肪肉瘤:一种罕见但独特的临床实体。
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引用本文的文献

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Defining "Giant" Mediastinal Tumors: Proposal of a New Clinical-Radiological Classification and Case Report.“巨大”纵隔肿瘤的定义:一种新的临床-放射学分类建议及病例报告
Diagnostics (Basel). 2025 Jan 12;15(2):159. doi: 10.3390/diagnostics15020159.
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Resection of a giant mediastinal liposarcoma by median sternotomy with vascular reconstruction-a case report.经正中胸骨切开术并进行血管重建切除巨大纵隔脂肪肉瘤——病例报告
Mediastinum. 2023 Aug 10;7:39. doi: 10.21037/med-23-20. eCollection 2023.
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Giant primary liposarcoma of the mediastinum: A case report and review of the literature.
纵隔原发性巨大脂肪肉瘤:一例报告并文献复习
SAGE Open Med Case Rep. 2023 Oct 16;11:2050313X231206031. doi: 10.1177/2050313X231206031. eCollection 2023.
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Imaging and Clinical Findings in a Series of Six Cases of Rare Primary Mediastinal Liposarcoma.6例罕见原发性纵隔脂肪肉瘤的影像学及临床特征
Radiol Cardiothorac Imaging. 2022 Mar 17;4(2):e210259. doi: 10.1148/ryct.210259. eCollection 2022 Apr.
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Multiple surgical excision for recurrent primary mediastinal liposarcoma.多次手术切除复发性原发性纵隔脂肪肉瘤。
Ann R Coll Surg Engl. 2021 Sep;103(8):e255-e258. doi: 10.1308/rcsann.2020.7115.
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Resection of a giant mediastinal atypical lipomatous tumor involving the esophagus.切除累及食管的巨大纵隔非典型脂肪瘤性肿瘤。
J Surg Case Rep. 2021 Jan 18;2021(1):rjaa561. doi: 10.1093/jscr/rjaa561. eCollection 2021 Jan.