Barbetakis N, Samanidis G, Paliouras D, Boukovinas I, Kiziridou A, Tsilikas C
Thoracic Surgery Department, Theagenio Cancer Hospital, Thessaloniki, Greece.
J BUON. 2008 Jul-Sep;13(3):429-31.
Liposarcoma is the most commonly diagnosed soft tissue sarcoma in adults and occurs predominantly in the lower limbs and retroperitoneum. Primary mediastinal liposarcomas are rare. Herein we report a case of a 68-year-old man with primary mediastinal liposarcoma involving the diaphragm and pericardium, which was successfully managed by complete surgical excision. The patient's postoperative course was uneventful with no evidence of recurrence 9 months after the operation. Surgical removal is the optimal treatment for a mediastinal liposarcoma, as it is in other sites. If the entire tumor can not be resected, surgical debulking often results in symptomatic relief. International literature suggests that recurrent disease occurs and therefore a long-term careful follow up is required.
脂肪肉瘤是成人中最常被诊断出的软组织肉瘤,主要发生在下肢和腹膜后。原发性纵隔脂肪肉瘤很罕见。在此,我们报告一例68岁男性原发性纵隔脂肪肉瘤累及膈肌和心包,通过完整手术切除成功治疗。患者术后恢复顺利,术后9个月无复发迹象。与其他部位一样,手术切除是纵隔脂肪肉瘤的最佳治疗方法。如果无法切除整个肿瘤,手术减瘤通常可缓解症状。国际文献表明会出现复发病例,因此需要长期密切随访。