Bouassida I, Pricopi C, Mangiameli G, Arame A, Auliac J B, Gorbatai B, Riquet M, Le Pimpec Barthes F
Service de chirurgie thoracique, université Paris-Descartes, hôpital Européen-Georges-Pompidou, 20, rue Leblanc, 75015 Paris, France.
Service de chirurgie thoracique, université Paris-Descartes, hôpital Européen-Georges-Pompidou, 20, rue Leblanc, 75015 Paris, France.
Rev Pneumol Clin. 2018 Sep;74(4):248-252. doi: 10.1016/j.pneumo.2018.03.009. Epub 2018 May 17.
Cardiac hydatid disease is uncommon and occurs in 0.5 to 2% of patients with hydatidosis. Isolated intrapericardial hydatid cystic disease is extremely rare.
We report the case of a young woman with cardiac compression due to multiple primary intrapericardial hydatid cysts. Since 1 year, she had gradual general health deterioration including dyspnoea, sweats and weight loss of 8kg. A widening of the mediastinum was observed on chest X-ray. The CT-scan, echocardiography and the dynamic IRM showed multiple mediastinal cysts with mass effect on the heart and main pulmonary artery. The size of the main pulmonary artery was reduced to 5 mm in diameter and the right upper pulmonary vein was nearly closed by posterior cysts. The right and left ventricular ejection fractions were estimated at about 34%. A complete resection of the cysts was performed by sternotomy. The surgical procedure was technically difficult because of major local inflammatory process. The postoperative outcome after an initial pulmonary embolism event was finally favourable.
Hydatidosis can lead to severe cardiac involvement. These rare forms of hydatid cystic disease must be known even in non endemic regions by surgeons because of increasing mobility of the world's population.
心脏包虫病并不常见,在包虫病患者中发生率为0.5%至2%。孤立性心包内包虫囊肿病极为罕见。
我们报告一例年轻女性患者,因多发性原发性心包内包虫囊肿导致心脏受压。一年来,她的整体健康状况逐渐恶化,包括呼吸困难、盗汗以及体重减轻8公斤。胸部X线检查发现纵隔增宽。CT扫描、超声心动图和动态磁共振成像显示多个纵隔囊肿,对心脏和主肺动脉有占位效应。主肺动脉直径缩小至5毫米,右上肺静脉几乎被后方囊肿闭塞。左右心室射血分数估计约为34%。通过胸骨切开术对囊肿进行了完整切除。由于局部存在严重炎症过程,手术操作在技术上具有难度。最初发生肺栓塞事件后,术后最终结果良好。
包虫病可导致严重的心脏受累。由于世界人口流动性增加,即使在非流行地区,外科医生也必须了解这些罕见的包虫囊肿病形式。