Savino Ketty, Bagliani Giuseppe, Crusco Federico, Padeletti Margherita, Lombardi Massimo
Cardiology and Cardiovascular Physiopathology, University of Perugia, Piazza Menghini, 1, Perugia 06129, Italy.
Arrhythmology Unit, Cardiology Department, Foligno General Hospital, Via Massimo Arcamone, Foligno 06034, Italy.
Card Electrophysiol Clin. 2018 Jun;10(2):413-429. doi: 10.1016/j.ccep.2018.02.011.
Cardiovascular imaging has radically changed the management of patients with arrhythmogenic cardiomyopathies. This article focuses on the role of echocardiography and MRI in the diagnosis of these structural diseases. Cardiomyopathies with hypertrophic pattern (hypertrophic cardiomyopathy, restrictive cardiomyopathies, amyloidosis, Anderson-Fabry disease, and sarcoidosis), cardiomyopathies with dilated pattern, inflammatory cardiac diseases, and right ventricular arrhythmogenic cardiomyopathy are analyzed. Finally, anatomic predictors of arrhythmias and sudden cardiac death are discussed. Each paragraph is attended by clinical cases that are discussed on the electrocardiogram, after integrated with the anatomic, functional, and hemodynamic modifications of cardiovascular imaging.
心血管成像已彻底改变了致心律失常性心肌病患者的管理方式。本文重点关注超声心动图和磁共振成像在这些结构性疾病诊断中的作用。分析了具有肥厚型模式的心肌病（肥厚型心肌病、限制型心肌病、淀粉样变性、安德森 - 法布里病和结节病）、扩张型模式的心肌病、炎症性心脏病以及右室致心律失常性心肌病。最后，讨论了心律失常和心源性猝死的解剖学预测因素。每段均伴有临床病例，这些病例在结合心血管成像的解剖、功能和血流动力学改变后，在心电图上进行讨论。
