Lei Wenjia, Sun Xue, Siddiqui Faiza Amber, Wang Yu, Zhang Ying
Department of Sonography, Shengjing Hospital of China Medical University, Shenyang, China.
Department of Entomology, The Pennsylvania State University, University Park, PA, USA.
Echocardiography. 2018 Jul;35(7):1063-1065. doi: 10.1111/echo.14029. Epub 2018 May 25.
Absent pulmonary valve syndrome (APVS) is a rare congenital cardiac anomaly characterized by hypoplastic or even absent pulmonary valve, to-and-fro flow across the pulmonary valve annulus, and dilatation of main pulmonary artery and branches. It is crucial to evaluate the degree of dilatation of pulmonary arteries and the presence of associated malformation and chromosomal anomalies affecting pregnancy decision. We described two- and three-dimensional (3D) echocardiographic findings of one fetus with APVS and indicated the beneficial contribution of 3D technology in understanding the anatomy.
肺动脉瓣缺如综合征（APVS）是一种罕见的先天性心脏畸形，其特征为肺动脉瓣发育不全甚至缺如、肺动脉瓣环处有往返血流以及主肺动脉及其分支扩张。评估肺动脉扩张程度以及是否存在影响妊娠决策的相关畸形和染色体异常至关重要。我们描述了一例患有APVS胎儿的二维和三维（3D）超声心动图检查结果，并指出3D技术在理解解剖结构方面的有益作用。
