• 文献检索
  • 文档翻译
  • 深度研究
  • 学术资讯
  • Suppr Zotero 插件Zotero 插件
  • 邀请有礼
  • 套餐&价格
  • 历史记录
应用&插件
Suppr Zotero 插件Zotero 插件浏览器插件Mac 客户端Windows 客户端微信小程序
定价
高级版会员购买积分包购买API积分包
服务
文献检索文档翻译深度研究API 文档MCP 服务
关于我们
关于 Suppr公司介绍联系我们用户协议隐私条款
关注我们

Suppr 超能文献

核心技术专利:CN118964589B侵权必究
粤ICP备2023148730 号-1Suppr @ 2026

文献检索

告别复杂PubMed语法,用中文像聊天一样搜索,搜遍4000万医学文献。AI智能推荐,让科研检索更轻松。

立即免费搜索

文件翻译

保留排版,准确专业,支持PDF/Word/PPT等文件格式,支持 12+语言互译。

免费翻译文档

深度研究

AI帮你快速写综述,25分钟生成高质量综述,智能提取关键信息,辅助科研写作。

立即免费体验

导致儿童致命性肠梗阻的肠旋转不良综合征。

Malrotation syndrome resulting in fatal ileus in children.

作者信息

Kernbach-Wighton Gerhard, Amberg Rainer, Madeal Burkhard

出版信息

Arch Kriminol. 2016 Sep;238(3-4):128-135.

PMID:29870176
Abstract

BACKGROUND

This report deals with two deaths of children involving intestinal volvulus, i. e. a pathological knotting and twisting of the mesenterial root on the basis of congenital malrotation followed by obstruction and extensive ischaenia.

CASE REPORTS

(1) A 10-year-old girl (premature, 25th week) with severe disability, amaurosis and epilepsy was admitted to hospital due to general agitation and a bloated abdomen without peristaltic sounds, but died some hours later. Autopsy revealed a volvulus of 2/3 of the small intestine based on congenital malrotation with additional clamping of the intestine underneath adhesions (previous appendectomy). The abdominal cavity showed beginning peritonitis as the cause of death. (2) A 2-month-old premature male baby (surviving twin, 29th week) with a persisting ductus arteriosus was hospitalised for four weeks after failed vascular surgery due to acute general deterioration. Radiological diagnostics using a contrast medium revealed a vascular anomaly (right-sided aortic arch). Around 10 hours later, the infant developed an acute abdomen with ileus symptoms. Emergency surgery showed infarction of the entire small intestine due to an anti-clockwise 180⁰-volvulus, with death occurring 24h later. Further examination showed a malrotation as anomaly. Apparently, the volvulus had been caused by extensive use of contrast medium resulting in increased intestinal mobility.

摘要

背景

本报告涉及两例儿童因肠扭转死亡的病例,即先天性肠旋转不良基础上肠系膜根部的病理性打结和扭转,随后出现梗阻和广泛缺血。

病例报告

(1)一名10岁女孩(早产,孕25周),重度残疾,失明且患有癫痫,因全身躁动和腹胀入院,无肠鸣音,数小时后死亡。尸检发现基于先天性肠旋转不良的小肠2/3肠扭转,且在粘连下方(既往阑尾切除术)肠管受压。腹腔显示早期腹膜炎为死因。(2)一名2个月大的早产男婴(存活双胞胎,孕29周),患有动脉导管未闭,因血管手术失败后急性全身状况恶化住院四周。使用造影剂的放射学诊断显示血管异常(右侧主动脉弓)。约10小时后,婴儿出现急腹症和肠梗阻症状。急诊手术显示由于逆时针180⁰肠扭转导致整个小肠梗死,24小时后死亡。进一步检查显示肠旋转不良为异常情况。显然,肠扭转是由于大量使用造影剂导致肠道活动增加所致。

相似文献

1
Malrotation syndrome resulting in fatal ileus in children.导致儿童致命性肠梗阻的肠旋转不良综合征。
Arch Kriminol. 2016 Sep;238(3-4):128-135.
2
[Two sudden deaths of children with mesenterium commune -- a case report].
Soud Lek. 2015;60(2):17-20.
3
Laparoscopic Treatment of Intestinal Malrotation in Children.小儿肠旋转不良的腹腔镜治疗
Eur J Pediatr Surg. 2016 Aug;26(4):376-81. doi: 10.1055/s-0035-1554914. Epub 2015 Jun 18.
4
Malrotation of Intestine with Carcinoma Colon in Adult.成人结肠恶性肿瘤伴肠旋转不良
JNMA J Nepal Med Assoc. 2014 Jan-Mar;52(193):726-8.
5
Diagnostic imaging of intestinal malrotation in association with other inborn malformations in children and adults--case presentations and a review of the literature on the subject.儿童和成人肠道旋转不良合并其他先天性畸形的诊断成像——病例报告及相关文献综述
Khirurgiia (Sofiia). 2014(3):37-45.
6
Volvulus of the entire small bowel with normal bowel fixation simulating malrotation and midgut volvulus.全小肠扭转,肠固定正常,模拟旋转不良和中肠扭转。
Pediatr Radiol. 2015 Dec;45(13):1953-6. doi: 10.1007/s00247-015-3430-9. Epub 2015 Jul 26.
7
Intestinal malrotation in Rubinstein-Taybi syndrome.鲁宾斯坦-泰比综合征中的肠旋转不良
Am J Med Genet A. 2015 Oct;167A(10):2399-401. doi: 10.1002/ajmg.a.37167. Epub 2015 Jun 19.
8
GIANT MORGAGNI HERNIA IN A FEMALE WITH MALROTATION SYNDROME AND THORACIC TRANSPOSITION OF SMALL BOWEL, COECUM, ASCENDING AND TRANSVERSE COLON.一名患有旋转不良综合征且小肠、盲肠、升结肠和横结肠发生胸腔内转位的女性的巨大莫尔加尼疝。
Khirurgiia (Sofiia). 2015;81(3):142-8.
9
"Milky" bowel and malrotation.“乳糜样”肠管与肠旋转不良
Surgery. 2017 Aug;162(2):468-469. doi: 10.1016/j.surg.2016.08.010. Epub 2016 Sep 22.
10
Gastric heterotopia with extensive involvement of the small intestine associated with congenital short bowel syndrome and intestinal malrotation.胃异位症广泛累及小肠,伴有先天性短肠综合征和肠旋转不良。
Fetal Pediatr Pathol. 2011;30(1):60-3. doi: 10.3109/15513815.2010.505631.