Salviz E A, Aksoy O, Bayazit E, Berkoz O, Evis S A, Tugrul K M
Acta Anaesthesiol Belg. 2016;67(4):191-195.
Epidermolysis bullosa (EB) is a rare genetic disease characterized by recurrent blister formation following injuries or traumas. In patients with EB, general anaesthesia may result in potential airway obstruction, aspiration and prolonged hospital stay due to airway instrumentation-associated new bullae formation and scarring. On the other hand, regional anaesthesia has been shown to be efficient and safe. Ultrasound (US)- guidance particularly provides additional benefits to this clinical situation by minimizing skin contacts, improving block success and preventing complications. We describe a patient with EB, whose bilateral pseudo-syndactyly surgical treatment was successfully managed by the use of US-guided axillary brachial plexus blocks.
大疱性表皮松解症（EB）是一种罕见的遗传性疾病，其特征为受伤或创伤后反复形成水疱。对于EB患者，全身麻醉可能会因气道器械操作相关的新水疱形成和瘢痕形成而导致潜在的气道梗阻、误吸及住院时间延长。另一方面，区域麻醉已被证明是有效且安全的。超声（US）引导尤其通过减少皮肤接触、提高阻滞成功率及预防并发症，为这种临床情况带来额外益处。我们描述了一名患有EB的患者，其双侧假性并指手术治疗通过使用超声引导下腋路臂丛神经阻滞得以成功实施。
