Liechti Rémy, Fourie Lana, Fischli Stefan, Metzger Jürg
Department of General and Visceral Surgery, Cantonal Hospital of Lucerne, Lucerne, Switzerland.
Department of Endocrinology, Cantonal Hospital of Lucerne, Lucerne, Switzerland.
J Surg Case Rep. 2018 May 18;2018(5):rjy106. doi: 10.1093/jscr/rjy106. eCollection 2018 May.
Lymphangiomas (LAs) are rare benign tumors of the lymphatic vessels. In total, 95% of all reported LAs are located in the head, neck and the mediastinum. LAs of the adrenal gland are very rare and currently, only ~54 cases have been reported in literature. We present a case of a big left-sided adrenal LA. Abdominal imaging revealed a big cystic lesion in the left upper abdomen of unknown origin. For diagnostic and therapeutic reasons we performed explorative midline laparotomy. The left adrenal gland was found to be the origin of the cystic tumor. Hence, the patient underwent adrenalectomy in order to remove the intact cystic lesion. Diagnosis was then confirmed by histological examination. With adrenal LAs being a very rare entity, diagnosis is challenging and only little evidence exists on treatment options. We discuss diagnostic, therapeutic and surgical approaches concerning such cases and provide an overview of the current literature.
淋巴管瘤（LAs）是淋巴管的罕见良性肿瘤。据报道，所有LAs中95%位于头颈部和纵隔。肾上腺淋巴管瘤非常罕见，目前文献中仅报道了约54例。我们报告一例巨大左侧肾上腺淋巴管瘤病例。腹部影像学检查显示左上腹有一个不明来源的巨大囊性病变。出于诊断和治疗目的，我们进行了中线剖腹探查术。发现左肾上腺是囊性肿瘤的起源。因此，患者接受了肾上腺切除术以切除完整的囊性病变。随后通过组织学检查确诊。由于肾上腺淋巴管瘤是一种非常罕见的疾病，诊断具有挑战性，关于治疗选择的证据很少。我们讨论此类病例的诊断、治疗和手术方法，并概述当前文献。
