Ma Jianbing, Zhang Weiqiang, Huang Yijuan, Wang Lizhang, Wang Jia, Yuan Linna, Zhang Jingfeng
Department of Radiology, the First Affiliated Hospital, College of Medicine, Jiaxing University, Jiaxing Department of Radiology, the First Affiliated Hospital, College of Medicine, Zhejiang University, Zhejiang Sheng, China.
Medicine (Baltimore). 2018 Jun;97(25):e11105. doi: 10.1097/MD.0000000000011105.
Primary pulmonary angiosarcoma is a rare disease. Here, we report the case of primary pulmonary angiosarcoma diagnosed computed tomographic pulmonary angiography (CTPA) and discuss its specific imaging characteristics.
A 46-year-old man was admitted for cough and shortness of breath. Thoracic CTPA images demonstrated a high-attenuation lesion surrounding by a halo sign in upper lobe of right lung, and the dilated vessel was also seen in lower lobe of right lung. The sign of "hillside sign" was observed on CTPA.
It was diagnosed with primary pulmonary angiosarcoma.
Right thoracotomy and right upper lobe lobectomy were performed.
Five years later, the patient dead of complete occlusion of the pulmonary artery owing to tumor recurrence.
Although primary pulmonary angiosarcoma is a rare disease with atypical early clinical symptoms, and it is often misdiagnosed as pulmonary embolism and pulmonary infection. Therefore, it is important to recognize the CTPA imaging characteristics of primary pulmonary angiosarcoma and Surgical resection should be performed to prolong the patients' lifetime.
原发性肺血管肉瘤是一种罕见疾病。在此，我们报告一例经计算机断层扫描肺血管造影（CTPA）诊断的原发性肺血管肉瘤病例，并讨论其特定的影像学特征。
一名46岁男性因咳嗽和呼吸急促入院。胸部CTPA图像显示右肺上叶有一个被晕征环绕的高密度病变，右肺下叶也可见扩张的血管。CTPA上观察到“山坡征”。
诊断为原发性肺血管肉瘤。
进行了右胸切开术和右上叶肺叶切除术。
五年后，患者因肿瘤复发导致肺动脉完全闭塞而死亡。
尽管原发性肺血管肉瘤是一种罕见疾病，早期临床症状不典型，常被误诊为肺栓塞和肺部感染。因此，认识原发性肺血管肉瘤的CTPA影像学特征很重要，应进行手术切除以延长患者寿命。
