孤立性右心室肥厚型心肌病。

Isolated Severe Right Ventricular Hypertrophic Cardiomyopathy.

机构信息

Department of Ultrasound, Union Hospital, Tongji Medical College, Huazhong University of Science and Technology, Wuhan, China; Hubei Province Key Laboratory of Molecular Imaging, Wuhan, China.

Department of Cardiovascular Surgery, Union Hospital, Tongji Medical College, Huazhong University of Science and Technology, Wuhan, China.

出版信息

Ann Thorac Surg. 2019 Jan;107(1):e23-e25. doi: 10.1016/j.athoracsur.2018.05.061. Epub 2018 Jun 23.

DOI:10.1016/j.athoracsur.2018.05.061

PMID:29944878

Abstract

A 26-year-old woman with a diagnosis of congenital heart disease was admitted to the hospital with exertional dyspnea, cyanotic complexion, and bilateral lower limb edema. All tests revealed isolated severe right ventricular hypertrophy. She was in poor condition, with a diminishing chance for routine surgical treatment, so she was scheduled for orthotopic homologous heart transplantation. After the operation, isolated severe right ventricular hypertrophic cardiomyopathy was confirmed histologically and pathologically. After the operation, the patient's cardiac function was normal. Exertional dyspnea, cyanotic complexion, and bilateral lower limb edema all improved postoperatively.

摘要

一位 26 岁的女性，患有先天性心脏病，因劳力性呼吸困难、发绀和双侧下肢水肿入院。所有检查均显示孤立性严重右心室肥厚。她的病情不佳，常规手术治疗的机会渺茫，因此安排了原位同种异体心脏移植。术后，组织病理学检查明确诊断为孤立性严重右心室肥厚型心肌病。术后，患者心功能正常。劳力性呼吸困难、发绀和双侧下肢水肿均在术后得到改善。