From the Centre de la main, Service de Chirurgie Plastique et de la Main, Département de l'Appareil Locomoteur, CHUV, Faculté de Biologie et Médecine, Université de Lausanne; the Division of Plastic and Reconstructive Surgery, Department of Surgery, and the Division of Musculoskeletal Imaging, Department of Medical Imaging, Faculty of Medicine, University of Toronto; and the Department of Clinical Imaging, Imperial College Healthcare NHS Trust.
Plast Reconstr Surg. 2018 Jul;142(1):148-151. doi: 10.1097/PRS.0000000000004455.
Lipomatosis of nerve is a rare, ill-defined, fibrofatty tumor intermingled among nerve fascicles. The classic presentation of lipomatosis of nerve describes focal distal involvement of the median nerve at the wrist. The purpose of this study was to determine the level of proximal lesion extension in cases of upper extremity lipomatosis of nerve using magnetic resonance imaging. The authors' study confirms that lipomatosis of nerve is more than a focal distal disease. Lipomatosis of nerve has the potential for multiple nerve involvement and for proximal nerve involvement extending to the nerve roots. Magnetic resonance imaging of the entire upper extremity may be indicated in patients with lipomatosis of nerve, especially when the ulnar nerve is affected.
神经脂肪瘤病是一种罕见的、定义不明确的纤维脂肪肿瘤，混杂在神经束之间。神经脂肪瘤病的典型表现为腕部正中神经的局限性远端受累。本研究旨在通过磁共振成像确定上肢神经脂肪瘤病的近端病变延伸程度。作者的研究证实，神经脂肪瘤病不仅仅是一种局限性远端疾病。神经脂肪瘤病可能涉及多根神经，并可能向神经根近端延伸。对于神经脂肪瘤病患者，尤其是尺神经受累的患者，可能需要进行整个上肢的磁共振成像检查。
