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一名49岁成年手部巨指症患者的手术治疗：病例报告

Surgical management of adult hand macrodactyly in a 49-year-old patient: A case report.

作者信息

Pang Chao-Jian, Huo Xiao-Yan, Liu Yuan, Yang Zong-You, Liu Lu, Fan Xiao-Bo, Xu Shang-Wen

机构信息

Department of Orthopaedic Surgery, The First Hospital of Handan, Handan 050000, Hebei Province, China.

Department of Orthopaedic Surgery, The Third Hospital of Hebei Medical University, Shijiazhuang 050000, Hebei Province, China.

出版信息

World J Clin Cases. 2024 Aug 6;12(22):5236-5244. doi: 10.12998/wjcc.v12.i22.5236.

DOI:10.12998/wjcc.v12.i22.5236
PMID:39109039
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC11238793/
Abstract

BACKGROUND

Macrodactyly is a rare congenital malformation characterized by an increase in the size of all structures of a digit, accounting for less than 1% of all congenital upper extremity conditions.

CASE SUMMARY

We report a case involving a 49-year-old woman who presented for the first time with untreated, radial-sided hand macrodactyly. We performed soft tissue debulking, amputation, median nerve neurotomy and coaptation, and carpal tunnel release. At the 6-year follow-up, no significant growth was observed in the bone or soft tissue of the affected area.

CONCLUSION

Tissue overgrowth in patients with progressive macrodactyly can continue and progress excessively with age. Median nerve neurotomy and coaptation play a crucial role in preventing recurrence of the deformity.

摘要

背景

巨指症是一种罕见的先天性畸形，其特征为手指所有结构的尺寸增大，在所有先天性上肢疾病中占比不到1%。

病例摘要

我们报告了一例49岁女性患者，她首次就诊时患有未经治疗的桡侧手部巨指症。我们进行了软组织减容、截肢、正中神经切断与吻合以及腕管松解术。在6年的随访中，患区的骨骼或软组织未观察到明显生长。

结论

进行性巨指症患者的组织过度生长会随着年龄的增长持续且过度发展。正中神经切断与吻合在预防畸形复发中起着关键作用。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/28c5/11238793/64b47fcdcae7/WJCC-12-5236-g007.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/28c5/11238793/4be47f1e11c1/WJCC-12-5236-g001.jpg
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https://cdn.ncbi.nlm.nih.gov/pmc/blobs/28c5/11238793/ff0a065ff48a/WJCC-12-5236-g003.jpg
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https://cdn.ncbi.nlm.nih.gov/pmc/blobs/28c5/11238793/5bdadfe139eb/WJCC-12-5236-g006.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/28c5/11238793/64b47fcdcae7/WJCC-12-5236-g007.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/28c5/11238793/4be47f1e11c1/WJCC-12-5236-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/28c5/11238793/a57d9c12b918/WJCC-12-5236-g002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/28c5/11238793/ff0a065ff48a/WJCC-12-5236-g003.jpg
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https://cdn.ncbi.nlm.nih.gov/pmc/blobs/28c5/11238793/64b47fcdcae7/WJCC-12-5236-g007.jpg

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