Lip Henry Tan Chor, Huei Tan Jih, Wahid Adrena Abdul, Vendargon Simon Jerome
Department of General Surgery, School of Medicine, National University of Malaysia Medical Centre, Kuala Lumpur, Malaysia.
Department of General Surgery, Hospital Sultanah Aminah, Johor Bahru, Malaysia.
Eurasian J Med. 2018 Jun;50(2):134-136. doi: 10.5152/eurasianjmed.2018.17388. Epub 2018 Jun 1.
Extrinsic pulmonary artery stenosis caused by anterior mediastinum teratoma presenting with an ejection systolic murmur is a rare phenomenon. Till date, 15 cases have been reported (inclusive of this case) in the English literatures. Herein we report a 20 year old female with extrinsic pulmonary artery stenosis because of compression by an anterior mediastinal teratoma with a loud ejection systolic murmur. The case report aims to highlight the awareness of such rare presentation of anterior mediastinal teratomas that may mimic congenital valvular heart diseases among clinicians.
前纵隔畸胎瘤导致的外在性肺动脉狭窄伴喷射性收缩期杂音是一种罕见现象。迄今为止,英文文献中已报道15例(包括本病例)。在此,我们报告一名20岁女性,因前纵隔畸胎瘤压迫导致外在性肺动脉狭窄,并伴有响亮的喷射性收缩期杂音。本病例报告旨在提高临床医生对前纵隔畸胎瘤这种可能酷似先天性瓣膜性心脏病的罕见表现的认识。