Fujii Masakuni, Saito Hiroaki, Shiode Junji
Department of Internal Medicine, Okayama Saiseikai General Hospital, 2-25 Kokutai-cho Kita-ku, Okayama, 700-8511, Japan.
Clin J Gastroenterol. 2019 Feb;12(1):38-45. doi: 10.1007/s12328-018-0883-z. Epub 2018 Jul 12.
There are no neuroectodermal cells in the gallbladder mucosa. Therefore, gallbladder neuroendocrine carcinoma (NEC) is extremely rare and has a poor prognosis. We report a case of a Japanese man in his 60s with this disease. The patient visited a family doctor for epigastralgia. Blood tests showed no abnormalities, including tumor markers, such as CEA and CA19-9. Abdominal ultrasonography (US) showed a low-echoic mass, 39 × 30 mm, with clear boundaries to the liver from the fundus of the gallbladder. Contrast-enhanced computed tomography showed that the tumor was enhanced early and washed out. Diffusion-weighted MRI showed a high signal. We suspected liver invasion of gallbladder cancer and performed a cholecystectomy, S4 and S5 hepatectomy, and lymphadenectomy. The resected whitish tumor was 29 × 22 mm. The tumor cells had honeycomb growth to the liver from the gallbladder. Tumor cells were poorly differentiated, and there was no stricture of the gland duct. Immunostaining showed that the tumor cells were positive for CD56, chromogranin A and synaptophysin, and about 30% were positive for Ki-67. Our diagnosis was gallbladder NEC with liver invasion. Although most malignant gallbladder tumors are adenocarcinomas, this case indicates that gallbladder NEC should be considered as a differential diagnosis of gallbladder tumor.
胆囊黏膜中不存在神经外胚层细胞。因此,胆囊神经内分泌癌(NEC)极为罕见,预后较差。我们报告一例60多岁患有此病的日本男性病例。该患者因上腹部疼痛就诊于家庭医生。血液检查未发现异常,包括癌胚抗原(CEA)和糖类抗原19-9(CA19-9)等肿瘤标志物。腹部超声(US)显示一个低回声肿块,大小为39×30毫米,从胆囊底部与肝脏界限清晰。增强计算机断层扫描显示肿瘤早期强化并呈廓清表现。扩散加权磁共振成像显示高信号。我们怀疑胆囊癌侵犯肝脏,遂行胆囊切除术、肝S4和S5段切除术以及淋巴结清扫术。切除的灰白色肿瘤大小为29×22毫米。肿瘤细胞呈从胆囊向肝脏的蜂窝状生长。肿瘤细胞分化差,且腺管无狭窄。免疫组化显示肿瘤细胞CD56、嗜铬粒蛋白A和突触素呈阳性,约30%的Ki-67呈阳性。我们的诊断为胆囊NEC伴肝脏侵犯。尽管大多数恶性胆囊肿瘤是腺癌,但该病例表明胆囊NEC应被视为胆囊肿瘤的鉴别诊断之一。