Mishra Ajit M, Prabhuraj A R, Pruthi Nupur, Rao Shilpa
Department of Neurosurgery, National Institute of Mental Health and Neurosciences, Bengaluru, Karnataka, India.
Department of Neuropathology, National Institute of Mental Health and Neurosciences, Bengaluru, Karnataka, India.
Surg Neurol Int. 2018 Jun 18;9:122. doi: 10.4103/sni.sni_117_18. eCollection 2018.
Intramedullary epidermoid cyst (IEC), typically associated with spinal dysraphism, is rare, with fewer than 80 such cases reported in the literature. Here we present an adult with an IEC without spinal dysraphism.
A 41-year-old female presented with the gradual onset of a progressive spastic paraparesis attributed to a magnetic resonance imaging (MRI)-documented D8-9 intramedullary lesion. Following microsurgical excision of the IEC, she fully recovered.
IECs are rare lesions, typically found in conjunction with spinal dysraphism. Utilizing MRI studies to document the lesion location, gross total microsurgical excision is the procedure of choice. Early excision of these benign lesions maximizes functional recovery.
髓内表皮样囊肿（IEC）通常与脊髓发育异常相关，较为罕见，文献报道的此类病例不足80例。本文报告1例无脊髓发育异常的成年IEC患者。
一名41岁女性因磁共振成像（MRI）显示的D8 - 9节段髓内病变，逐渐出现进行性痉挛性截瘫。经显微手术切除IEC后，患者完全康复。
IEC是罕见病变，通常与脊髓发育异常并存。利用MRI检查确定病变位置，显微手术全切是首选治疗方法。早期切除这些良性病变可使功能恢复最大化。
