Graillon T, Rakotozanany P, Meyer M, Dufour H, Fuentes S
Service de neurochirurgie, Pr-Dufour hôpital La Timone adultes, Aix-Marseille université, AP-HM, 264, rue St-Pierre, 13005 Marseille, France.
Service de neurochirurgie, Pr-Dufour hôpital La Timone adultes, Aix-Marseille université, AP-HM, 264, rue St-Pierre, 13005 Marseille, France.
Neurochirurgie. 2017 May;63(2):99-102. doi: 10.1016/j.neuchi.2017.01.004. Epub 2017 May 8.
Epidermoid cysts are classical tumors in neurosurgery, but spinal locations are rare and intramedullary locations represent only approximately 80 cases in the literature. Intramedullary epidermoid cysts arise from ectodermic tissue inclusion during neural tube closure. Intramedullary epidermoid cysts are more frequent in young patients and in a thoracic location. We report the case of a 61-year-old patient consulting for bilateral asymmetrical progressive paraparesis and proprioceptive ataxia revealing a T3-T4 exophytic medullar epidermoid cyst. The tumor was surgically removed with a favorable outcome. The capsule was partially removed. The authors present an updated literature review of intramedullary epidermoid cyst diagnosis, management and recommendations.
表皮样囊肿是神经外科的经典肿瘤，但在脊柱部位较为罕见，而髓内部位在文献中仅约有80例报道。髓内表皮样囊肿起源于神经管闭合期间的外胚层组织包涵物。髓内表皮样囊肿在年轻患者和胸段更为常见。我们报告了一例61岁患者，因双侧不对称性进行性截瘫和本体感觉共济失调前来就诊，检查发现为T3 - T4节段髓外生性表皮样囊肿。该肿瘤经手术切除，预后良好。囊肿包膜部分切除。作者对髓内表皮样囊肿的诊断、治疗及建议进行了最新的文献综述。
