Alimli Ayse Gul, Ucar Murat, Oztunali Cigdem, Akkan Koray, Boyunaga Oznur, Damar Cagrı, Derinkuyu Betül, Tokgöz Nil
Gazi University School of Medicine, TR.
J Belg Soc Radiol. 2016 Jun 1;100(1):63. doi: 10.5334/jbr-btr.1090.
Juvenile nasopharyngeal angiofibroma (JNA) is a rare tumor that exhibits a predictable spreading pattern. Radiologist's prior knowledge on the tumor's characteristics aids in establishing a diagnosis. We aimed to report the characteristic Magnetic Resonance Imaging (MRI) findings and the spread patterns of JNA.
We retrospectively evaluated the MRI findings and extension pathways of 6 cases of JNA.
The patients' age ranged from 8 to 16 years and all patients were male. The tumors were classified according to the Onerci system. Tumors were largely isointense to muscle on T1-weighted images and hyperintense on T2-weighted images. All lesions had internal signal-void regions and all exhibited intense enhancement after IV contrast injection. Diffusion restriction was not an associated feature. ADC values for these tumors were high. The evaluation of the available MR angiography studies of three patients showed the blood supply to the tumor to be mainly from the internal maxillary branch of the external carotid artery. In all patients, the diagnosis was based on MR images and a surgical excision was planned.
The diagnosis can be established based on the characteristic imaging findings and the clinical history without performing a biopsy.
青少年鼻咽血管纤维瘤（JNA）是一种罕见肿瘤，具有可预测的扩散模式。放射科医生对该肿瘤特征的先验知识有助于做出诊断。我们旨在报告JNA的特征性磁共振成像（MRI）表现及扩散模式。
我们回顾性评估了6例JNA的MRI表现及扩展途径。
患者年龄为8至16岁，均为男性。肿瘤根据奥内尔奇系统进行分类。肿瘤在T1加权图像上与肌肉大致等信号，在T2加权图像上呈高信号。所有病变均有内部信号缺失区域，静脉注射造影剂后均表现出明显强化。扩散受限并非相关特征。这些肿瘤的表观扩散系数（ADC）值较高。对3例患者的现有磁共振血管造影研究评估显示，肿瘤血供主要来自颈外动脉的上颌内分支。所有患者均根据磁共振图像做出诊断，并计划进行手术切除。
无需进行活检，基于特征性影像学表现和临床病史即可做出诊断。
