Department of Otolaryngology, Kaohsiung Chang Gung Memorial Hospital, Chang Gung University College of Medicine, Kaohsiung, Taiwan.
Department of Anatomic Pathology, Kaohsiung Chang Gung Memorial Hospital, Chang Gung University College of Medicine, Kaohsiung, Taiwan.
Head Neck. 2018 Sep;40(9):E91-E95. doi: 10.1002/hed.25338. Epub 2018 Jul 26.
Sinonasal renal cell-like adenocarcinoma is rare and exhibits unique pathological and clinical manifestations. Correct diagnosis and treatment of this newly described entity are challenging for both clinicians and pathologists.
We report a female patient with sinonasal renal cell-like adenocarcinoma who initially presented with right intermittent epistaxis.
A 26-year-old woman presented with a 1-year history of right intermittent epistaxis and hyposmia. Nasal endoscopy revealed a reddish tumor in the right nasal cavity. An MRI revealed a hyperintense tumor arising from the right olfactory cleft accompanied by prominent feeding vessels originating from the anterior ethmoid artery (AEA). We performed a bicoronal incision with ligation of the AEA followed by endoscopic resection of the skull base tumor. The patient is currently free of recurrence.
This is the first study to review the clinical features of sinonasal renal cell-like adenocarcinoma. We recommend surgical resection as the mainstay of treatment.
鼻腔鼻窦肾细胞样腺癌较为罕见，具有独特的病理和临床表现。对于临床医生和病理学家来说，正确诊断和治疗这种新描述的实体具有挑战性。
我们报告了一名女性鼻腔鼻窦肾细胞样腺癌患者，她最初表现为右侧间歇性鼻出血。
一名 26 岁女性因右侧间歇性鼻出血和嗅觉减退 1 年就诊。鼻内镜检查显示右侧鼻腔有一个红色肿瘤。MRI 显示起源于右侧嗅裂的高信号肿瘤，伴有来自前筛动脉（AEA）的突出供血血管。我们进行了冠状切口结扎 AEA，然后经鼻内镜切除颅底肿瘤。患者目前无复发。
这是第一项回顾鼻腔鼻窦肾细胞样腺癌临床特征的研究。我们建议手术切除作为主要治疗方法。
