Houari N, Touzani S, Salhi H, Alaoui Lamrani M-Y, Ibnmajdoub K, El Ouahabi H, El Bouazzaoui A, Boukatta B, Maâroufi M, Maazaz K, Kanjaa N
Anesthesiology & Intensive Care Unit A4, Hassan II University Hospital, Fez, Morocco.
Endocrinology Department, Hassan II University Hospital, Fez, Morocco.
Case Rep Crit Care. 2018 Jul 5;2018:4058046. doi: 10.1155/2018/4058046. eCollection 2018.
Catecholamine-induced cardiogenic shock is a rare manifestation of paragangliomas. The high mortality rate of this condition makes the immediate, multidisciplinary approach mandatory.
We report a case of an 18-year-old woman with a retroperitoneal secreting paraganglioma, complicated with a cardiogenic shock and an acute adrenergic myocarditis, requiring hemodynamic support and emergency arterial embolization prior to surgical excision, with a favorable outcome.
Paraganglioma-induced myocarditis is rare but can be dramatic. Management requires appropriate and immediate hemodynamic support. Embolization may be an alternative to stabilize the patient prior to surgery.
儿茶酚胺诱导的心源性休克是副神经节瘤的一种罕见表现。这种情况的高死亡率使得立即采取多学科方法成为必要。
我们报告一例18岁女性患者,患有腹膜后分泌性副神经节瘤,并发心源性休克和急性肾上腺素能心肌炎,在手术切除前需要血流动力学支持和紧急动脉栓塞,结果良好。
副神经节瘤诱导的心肌炎罕见但可能很严重。治疗需要适当且立即的血流动力学支持。栓塞可能是在手术前稳定患者病情的一种替代方法。