Department of Radiology, University of Colorado Anschutz Medical Campus, Aurora, CO, USA.
Department of Radiology, Children's Hospital Colorado, Aurora, CO, USA.
Br J Radiol. 2019 Jan;92(1093):20180185. doi: 10.1259/bjr.20180185. Epub 2018 Aug 31.
Congenital pulmonary artery anomalies represent a diverse group of abnormalities, ranging from asymptomatic incidental findings to causes of sudden cardiac death. While some may be recognized in childhood, others may be found incidentally in adulthood. We review the clinical and imaging findings in patients with congenital anomalies of the pulmonary arteries, including valvular and perivavular anomalies as well as abnormal narrowing, course and communications of the pulmonary arteries. We also discuss the role of various imaging modalities in the evaluation of these patients. It is vital to be aware of the key radiologic manifestations and associated haemodynamic consequences in these conditions in order to facilitate accurate diagnosis and prognostic stratification.
先天性肺动脉异常是一组表现多样的病变，从无症状的偶然发现到引起心源性猝死不等。有些病变可能在儿童期被识别，而另一些病变可能在成年期偶然发现。我们回顾了患有肺动脉先天性异常患者的临床和影像学表现，包括瓣叶和瓣周异常以及肺动脉狭窄、走行和交通异常。我们还讨论了各种影像学检查在这些患者评估中的作用。了解这些疾病的关键放射学表现和相关血流动力学后果对于准确诊断和预后分层至关重要。
