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一名40岁无症状男性的四叶式主动脉瓣:病例报告

A quadricuspid aortic valve in an asymptomatic 40-year-old man: a case report.

作者信息

Pasanisi Giovanni, Mazzanti Gaia, Sassone Biagio

机构信息

Department of Emergency, Division of Cardiology, Delta Hospital, Azienda Unità Sanitaria Locale di Ferrara, Ferrara, Italy.

Unità Operativa di Cardiologia, Ospedale del Delta, Azienda Unità Sanitaria Locale di Ferrara, Via Valle Oppio 2, 44023 Lagosanto, Ferrara, Italy.

出版信息

J Med Case Rep. 2018 Aug 16;12(1):234. doi: 10.1186/s13256-018-1755-3.

Abstract

BACKGROUND

Integrated transthoracic and transesophageal echocardiography enables identification and characterization of a quadricuspid aortic valve anomaly.

CASE PRESENTATION

A totally asymptomatic 40-year-old white man was referred to our Division of Cardiology after accidental finding of a heart murmur. Transesophageal echocardiography detected a quadricuspid aortic valve characterized by four cusps of equal size and severe aortic valvular regurgitation, without any further anomalies. He underwent a successful aortic valve repair.

CONCLUSIONS

Quadricuspid aortic valve anomaly is a rare congenital cardiac defect that can cause progressive valvular complications.

摘要

背景

经胸和经食管超声心动图联合检查能够识别和描述四叶式主动脉瓣异常。

病例介绍

一名40岁完全无症状的白人男性在意外发现心脏杂音后被转诊至我们的心脏病科。经食管超声心动图检测到一个四叶式主动脉瓣,其特点是四个瓣叶大小相等且存在严重的主动脉瓣反流,无其他异常。他接受了成功的主动脉瓣修复手术。

结论

四叶式主动脉瓣异常是一种罕见的先天性心脏缺陷,可导致进行性瓣膜并发症。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/be6d/6094910/ce1cc52312d2/13256_2018_1755_Fig1_HTML.jpg

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