Di Giacomo Paola, Celli Mauro, Ierardo Gaetano, Polimeni Antonella, Di Paolo Carlo
Department of Oral and Maxillofacial Sciences, Policlinico Umberto I, "Sapienza" University of Rome, Rome, Italy.
Department of Rare Diseases, Policlinico Umberto I, "Sapienza" University of Rome, Rome, Italy.
J Int Soc Prev Community Dent. 2018 Jul-Aug;8(4):333-338. doi: 10.4103/jispcd.JISPCD_103_18. Epub 2018 Jul 18.
The objective of this study is to recognize representative cranio-cervico-mandibular features of patients with Ehler-Danlos syndrome and associated temporomandibular disorders (TMDs), to assess a targeted and integrated treatment plan.
After a diagnosis of disease, 38 individiuals with Ehler-Danlos syndrome and temporomandibular symptomatology referred were evaluated. Gnathological evaluation, according to the Diagnostic Criteria for TMDs, and radiographic imaging was performed. In addition, digital evaluation of occlusal and muscular balance, using surface electromyography of jaw muscles, was conducted. Statistical software for data analysis - STATA (StataCorp, College station, Texas, USA) - was used.
Most common temporomandibular dysfunctions were arthralgia, myalgia, disc displacement with reduction and subluxation. Headache and neck pain were the most frequent comorbidities. Somatization, depression, anxiety, and obsessive-compulsive behavior were the most recurrent psychological disorders. Electromyographic analysis showed out of normal range data.
Early diagnosis and interception are requested to avoid injuries and repeated traumatism. Multidisciplinary treatments are available to approach all the aspects of the syndrome.
本研究的目的是识别患有埃勒斯-当洛综合征及相关颞下颌关节紊乱病（TMDs）患者的典型颅颈下颌特征，评估针对性的综合治疗方案。
在确诊疾病后，对38例患有埃勒斯-当洛综合征且有颞下颌症状的转诊患者进行了评估。根据TMDs的诊断标准进行了颌学评估，并进行了影像学检查。此外，还使用颌面部肌肉的表面肌电图对咬合和肌肉平衡进行了数字化评估。使用数据分析统计软件——STATA（美国德克萨斯州大学城的StataCorp公司）进行分析。
最常见的颞下颌功能障碍是关节痛、肌痛、可复性盘移位和半脱位。头痛和颈部疼痛是最常见的合并症。躯体化、抑郁、焦虑和强迫行为是最常见的心理障碍。肌电图分析显示数据超出正常范围。
需要早期诊断和干预以避免损伤和反复创伤。可采用多学科治疗方法来处理该综合征的各个方面。
