miRagen Therapeutics, Inc., Boulder, CO, USA.
Section of Dermatopathology, Department of Pathology, Department of Translational and Molecular Pathology, The University of Texas MD Anderson Cancer Center, Houston, TX, USA.
Br J Haematol. 2018 Nov;183(3):428-444. doi: 10.1111/bjh.15547. Epub 2018 Aug 20.
miR-155, a microRNA associated with poor prognosis in lymphoma and leukaemia, has been implicated in the progression of mycosis fungoides (MF), the most common form of cutaneous T-cell lymphoma (CTCL). In this study, we developed and tested cobomarsen (MRG-106), a locked nucleic acid-modified oligonucleotide inhibitor of miR-155. In MF and human lymphotropic virus type 1 (HTLV-1+) CTCL cell lines in vitro, inhibition of miR-155 with cobomarsen de-repressed direct miR-155 targets, decreased expression of multiple gene pathways associated with cell survival, reduced survival signalling, decreased cell proliferation and activated apoptosis. We identified a set of genes that are significantly regulated by cobomarsen, including direct and downstream targets of miR-155. Using clinical biopsies from MF patients, we demonstrated that expression of these pharmacodynamic biomarkers is dysregulated in MF and associated with miR-155 expression level and MF lesion severity. Further, we demonstrated that miR-155 simultaneously regulates multiple parallel survival pathways (including JAK/STAT, MAPK/ERK and PI3K/AKT) previously associated with the pathogenesis of MF, and that these survival pathways are inhibited by cobomarsen in vitro. A first-in-human phase 1 clinical trial of cobomarsen in patients with CTCL is currently underway, in which the panel of proposed biomarkers will be leveraged to assess pharmacodynamic response to cobomarsen therapy.
miR-155 是一种与淋巴瘤和白血病不良预后相关的 microRNA,已被牵涉到蕈样肉芽肿(MF)的进展中,MF 是最常见的皮肤 T 细胞淋巴瘤(CTCL)。在这项研究中,我们开发并测试了 cobomarsen(MRG-106),这是一种 miR-155 的锁核酸修饰的寡核苷酸抑制剂。在 MF 和人类嗜 T 淋巴细胞病毒 1(HTLV-1+)CTCL 细胞系中,cobomarsen 抑制 miR-155 会去抑制 miR-155 的直接靶标,降低与细胞存活相关的多个基因途径的表达,减少存活信号,降低细胞增殖并激活凋亡。我们确定了一组受 cobomarsen 显著调节的基因,包括 miR-155 的直接和下游靶标。使用 MF 患者的临床活检,我们证明了这些药效动力学生物标志物在 MF 中表达失调,与 miR-155 的表达水平和 MF 病变严重程度相关。此外,我们证明 miR-155 同时调节多个平行的存活途径(包括 JAK/STAT、MAPK/ERK 和 PI3K/AKT),这些途径以前与 MF 的发病机制有关,而 cobomarsen 在体外抑制这些存活途径。目前正在进行 cobomarsen 治疗 CTCL 患者的首次人体 1 期临床试验,其中拟议的生物标志物将被利用来评估对 cobomarsen 治疗的药效动力学反应。