Large Aneurysm in Renal Angiomyolipoma.

Large aneurysms seen in renal angiomyolipoma are usually more common in patients with tuberous sclerosis in comparison with sporadic cases and they are more prone to hemorrhage ranging from renal hematoma to life-threatening perirenal hemorrhages. We present a case of 13-year female patient who was referred to Civil Hospital, Karachi, with bilateral flank pain, cutaneous nodule and low intelligence. Her color doppler ultrasound revealed pseudoaneurysm in left kidney on the background of bilateral renal angiomyolipomas. Contrast enhanced CT scan confirmed various radiological manifestations of tuberous sclerosis including subependymal tubers, bilateral angiomyolipomas, and pseudoaneurysm associated with perinephric hemorrhage in left kidney.