Cammarota T, Fauciglietti P, Sarno A, Bundino S, Bonvicino A, Regge D
Servizio di Radiologia, Ospedale S. Lazzaro, USSL VIII, Molinette, Torino.
Minerva Urol Nefrol. 1995 Mar;47(1):5-8.
The authors describe a case of 21-year-old man suffering from tuberous sclerosis, more than once operated for subependymal astrocytomas, presenting multiple bilateral renal angiomyolipomas of 1.5 cm as greatest diameter. Last abdominal ultrasonographic exam, done a few years after the former, revealed an angiomyolipoma measuring 10 cm in diameter at the upper pole of the right kidney. This angiomyolipoma projected into a large haematoma of 15 cm in diameter, absolutely asymptomatic. After CT control bone lesions were removed. This case shows the progressive increase in number and size of renal angiomyolipomas, with subsequent haemorrhagic complications, suggesting as opportune periodic ultrasonographic controls.
作者描述了一例21岁患有结节性硬化症的男性患者,曾多次接受室管膜下星形细胞瘤手术,双侧肾脏出现多个最大直径为1.5厘米的肾血管平滑肌脂肪瘤。前一次检查几年后的最后一次腹部超声检查显示,右肾上极有一个直径10厘米的肾血管平滑肌脂肪瘤。这个肾血管平滑肌脂肪瘤突入一个直径15厘米的巨大血肿中,完全没有症状。经CT检查后切除了骨病变。该病例显示肾血管平滑肌脂肪瘤的数量和大小逐渐增加,随后出现出血并发症,提示定期进行超声检查是合适的。