Voss Jan Oliver, Buehling Salvatore, Thieme Nadine, Doll Christian, Hauptmann Kathrin, Heiland Max, Adolphs Nicolai, Raguse Jan-Dirk
Charité - Universitätsmedizin Berlin, Corporate Member of Freie Universität Berlin, Humboldt-Universität zu Berlin, Berlin Institute of Health, Department of Oral and Maxillofacial Surgery, Augustenburger Platz 1, 13353, Berlin, Germany.
Charité - Universitätsmedizin Berlin, Corporate Member of Freie Universität Berlin, Humboldt-Universität zu Berlin, Berlin Institute of Health, Diagnostic and Interventional Radiology and Nuclear Medicine, Augustenburger Platz 1, 13353, Berlin, Germany.
Int J Pediatr Otorhinolaryngol. 2018 Oct;113:260-265. doi: 10.1016/j.ijporl.2018.07.055. Epub 2018 Aug 2.
Congenital cysts and fistulas of the neck are common in children, often located in the head and neck area. Belonging to the group of tumor-like conditions, dermoid and epidermoid cysts are dysontogenetic lesions with seldom multiple co-occurrences in infants.
We report on a nine-month-old female with a persisting congenital fistula of the tongue. The patient was admitted with acute poor feeding and hypersalivation, which started within the last 24 h. Magnetic resonance imaging detected a fistula of the tongue connected to sublingual cystic lesions. Intraoral surgical removal of three cystic lesions and the fistula was performed under general anesthesia. Histopathological analysis confirmed the coexistence of an epidermoid cyst and two dermoid cysts.
Sudden feeding difficulties in combination with dysphagia and tongue displacement in pediatric patients pose an emergency situation that requires prompt diagnostic clarification. A persisting congenital fistula of the tongue is a clear indication of dysontogenetic lesions, including malformations, tumors, and tumor-like lesions. Congenital sublingual cysts are rare in infants, but can be life threatening when present. Surgical excision with histopathological analysis is essential to exclude any form of malignancy and malignant transformation.
先天性颈部囊肿和瘘管在儿童中很常见,通常位于头颈部区域。皮样囊肿和表皮样囊肿属于肿瘤样病变,在婴儿中很少多发。
我们报告了一名9个月大的患有持续性先天性舌瘘的女性患者。患者因急性喂养困难和流涎过多入院,症状在过去24小时内开始出现。磁共振成像检测到与舌下囊性病变相连的舌瘘。在全身麻醉下进行了口腔内手术切除三个囊性病变和瘘管。组织病理学分析证实存在一个表皮样囊肿和两个皮样囊肿。
小儿患者出现突然的喂养困难并伴有吞咽困难和舌移位是一种紧急情况,需要迅速进行诊断明确。持续性先天性舌瘘明确提示发育异常性病变,包括畸形、肿瘤和肿瘤样病变。先天性舌下囊肿在婴儿中罕见,但一旦出现可能危及生命。手术切除并进行组织病理学分析对于排除任何形式的恶性肿瘤和恶性转化至关重要。