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发作性睡病 1 型中的假性。

Pseudo in Narcolepsy Type 1.

机构信息

Mayo Clinic, Rochester, Minnesota.

出版信息

J Clin Sleep Med. 2018 Sep 15;14(9):1625-1627. doi: 10.5664/jcsm.7350.

DOI:10.5664/jcsm.7350
PMID:30176979
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC6134240/
Abstract

The rare constellation of multiple episodes of cataplexy that are refractory to therapy is called . We describe a young adult with known narcolepsy type 1 who reported a marked exacerbation of her symptoms that was initially suspicious for . Neurological evaluation, polysomnography, and additional history revealed that the spells were not consistent with cataplexy, but rather with a somatoform disorder. The case highlights the importance of considering psychosomatic factors in narcolepsy type 1 when presumed cataplexy remains suboptimally controlled despite adequate dosing with appropriate medications.

摘要

这种罕见的多发性猝倒症,即使经过治疗也无法缓解,被称为难治性猝倒症。我们描述了一位年轻的成年患者,她患有已知的 1 型发作性睡病,报告称其症状明显恶化,最初怀疑是难治性猝倒症。神经学评估、多导睡眠图和其他病史显示,这些发作与猝倒症不一致,而是与躯体形式障碍有关。该病例强调了在 1 型发作性睡病患者中,当假定的猝倒症尽管使用适当的药物进行了充分的剂量治疗,但仍未得到最佳控制时,考虑心身因素的重要性。

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Pseudo in Narcolepsy Type 1.发作性睡病 1 型中的假性。
J Clin Sleep Med. 2018 Sep 15;14(9):1625-1627. doi: 10.5664/jcsm.7350.
2
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[Integrated treatment of the symptoms of narcolepsy-cataplexy syndrome with sodium oxybate].[用羟丁酸钠综合治疗发作性睡病-猝倒综合征的症状]
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引用本文的文献

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Recognizing the Symptom Spectrum of Narcolepsy to Improve Timely Diagnosis: A Narrative Review.认识发作性睡病的症状谱以改善及时诊断:一项叙述性综述。
Nat Sci Sleep. 2021 Jul 7;13:1083-1096. doi: 10.2147/NSS.S278046. eCollection 2021.

本文引用的文献

1
Narcolepsy and Other Central Hypersomnias.发作性睡病及其他中枢性过度嗜睡症
Continuum (Minneap Minn). 2017 Aug;23(4, Sleep Neurology):989-1004. doi: 10.1212/CON.0000000000000492.
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Treatment paradigms for cataplexy in narcolepsy: past, present, and future.发作性睡病中猝倒的治疗模式:过去、现在与未来。
Nat Sci Sleep. 2015 Dec 11;7:159-69. doi: 10.2147/NSS.S92140. eCollection 2015.
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Status cataplecticus as initial presentation of late onset narcolepsy.猝倒发作作为迟发性发作性嗜睡症的初始表现。
J Clin Sleep Med. 2014 Feb 15;10(2):207-9. doi: 10.5664/jcsm.3456.
4
Status cataplecticus precipitated by abrupt withdrawal of venlafaxine.文拉法辛突然停药诱发的僵住状态。
J Clin Sleep Med. 2013 Jul 15;9(7):715-6. doi: 10.5664/jcsm.2848.
5
Pseudocataplexy and transient functional paralysis: a spectrum of psychogenic motor disorder.假性猝倒和一过性功能性瘫痪:心因性运动障碍谱。
J Neuropsychiatry Clin Neurosci. 2010 Fall;22(4):445-50. doi: 10.1176/jnp.2010.22.4.445.
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Pseudocataplexy in narcolepsy with cataplexy.伴猝倒发作的发作性睡病中的假性猝倒。
Sleep Med. 2010 Jun;11(6):591-4. doi: 10.1016/j.sleep.2010.03.004. Epub 2010 May 14.
7
Exacerbation of cataplexy following gradual withdrawal of antidepressants: manifestation of probable protracted rebound cataplexy.抗抑郁药逐渐撤药后猝倒症状加重:可能为持续性反弹猝倒的表现。
Sleep Med. 2009 Apr;10(4):416-21. doi: 10.1016/j.sleep.2008.04.004. Epub 2008 Aug 26.
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Status cataplecticus leading to the obstetric complication of prolonged labor.
J Clin Sleep Med. 2007 Feb 15;3(1):56-7.
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Reevaluating spells initially identified as cataplexy.
Sleep Med. 2005 Nov;6(6):537-42. doi: 10.1016/j.sleep.2005.04.006. Epub 2005 Jul 5.
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Pseudocataplexy.发作性睡病猝倒症样发作
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