Vela José I, Marcantonio Ivanna, Díaz-Cascajosa Jesús, Crespí Jaume, Buil José A
Department of Ophthalmology, Hospital de la Santa Creu i de Sant Pau, Barcelona, Spain.
Department of Ophthalmology, Institut Condal d'Oftalmología, Barcelona, Spain.
BMC Ophthalmol. 2018 Sep 10;18(1):242. doi: 10.1186/s12886-018-0814-2.
To report our findings in a young patient with unilateral retinitis pigmentosa (RP)-like appearance who developed pigmentary changes in his left retina after an episode of bilateral pars planitis.
A 17-year-old man presented with 6 months of blurry vision in both eyes. He was diagnosed with bilateral pars planitis. Progressive, intraretinal bone crepuscule pigmentation developed in his left retina during the following three months. An electroretinogram showed subnormal response only in the left eye, suggesting the diagnosis of unilateral pseudoRP.
An inflammatory disease like pars planitis can accelerate the pigmentation of the retina and mimic a RP in young patients. Causes of pseudoRP may be considered, especially in those rare cases with unilateral affection.
报告我们在一名年轻患者中的发现,该患者有单侧视网膜色素变性(RP)样外观,在双侧睫状体平坦部炎发作后左眼出现色素变化。
一名17岁男性出现双眼视力模糊6个月。他被诊断为双侧睫状体平坦部炎。在接下来的三个月里,他的左眼视网膜出现了进行性的视网膜内骨小体色素沉着。视网膜电图显示仅左眼反应异常,提示诊断为单侧假性RP。
像睫状体平坦部炎这样的炎症性疾病可加速视网膜色素沉着,并在年轻患者中模拟RP。可能需要考虑假性RP的病因,尤其是在那些单侧受累的罕见病例中。