Börekci Ali, Kuru Bektaşoğlu Pınar, Ramazanoğlu Ali Fatih, Gürer Bora, Çelikoğlu Erhan
Turkish Ministry of Health, University of Health Sciences, Fatih Sultan Mehmet Education and Research Hospital, Department of Neurosurgery, Istanbul, Turkey.
Turkish Ministry of Health, University of Health Sciences, Fatih Sultan Mehmet Education and Research Hospital, Department of Neurosurgery, Istanbul, Turkey; Marmara University School of Medicine, Department of Physiology, Istanbul, Turkey.
Neurol Neurochir Pol. 2018 Nov-Dec;52(6):670-676. doi: 10.1016/j.pjnns.2018.09.001. Epub 2018 Sep 11.
Liponeurocytomas are mostly localized in cerebellar hemispheres and the second most common location is the vermis. It is rarely observed within the intracranial ventricles. Here, we present a case of liponeurocytoma located in the right lateral ventricle and the systematic review of the literature.
We searched PubMed with keyword 'central liponeurocytoma' and the references of the related articles. There were no language or year restrictions. We included articles focusing on liponeurocytomas located in the central nervous system leaving a total of 17 articles and 21 reported cases.
A 62-year-old female presented with confusion and mental disorientation without any other neurological deficit. Her magnetic resonance imaging (MRI) revealed a lateral ventricle located mass lesion which was hypointense on T1-weighted images (WI) and heterogeneously hyperintense on T2-WI with cystic component. Via craniotomy, yellow-beige colored, soft and moderately vascularized mass lesion was gross totally resected. Despite postoperative MRI revealed total resection, patient had left-sided hemiparesis. The patient recovered well in her postoperative period and there was no recurrence on her 6th month follow-up MRI.
Intraventricular liponeurocytoma has a favorable clinical course, and radiological features may be useful in the diagnosis of this rare tumor before surgery. Supratentorial intraventricular location should be kept in mind in the differential diagnosis of the lateral ventricular tumors.
脂肪神经细胞瘤大多位于小脑半球，第二常见的部位是蚓部。在颅内脑室中很少见到。在此，我们报告一例位于右侧脑室的脂肪神经细胞瘤病例并对文献进行系统综述。
我们在PubMed上以“中枢性脂肪神经细胞瘤”为关键词进行检索，并查阅相关文章的参考文献。检索没有语言或年份限制。我们纳入了聚焦于中枢神经系统脂肪神经细胞瘤的文章，共17篇文章和21例报告病例。
一名62岁女性出现意识模糊和精神定向障碍，无任何其他神经功能缺损。她的磁共振成像（MRI）显示侧脑室有一个占位性病变，在T1加权像（WI）上呈低信号，在T2加权像上呈不均匀高信号且有囊性成分。通过开颅手术，将黄米色、质地柔软且血管化程度中等的占位性病变整块全切。尽管术后MRI显示全切，但患者出现了左侧偏瘫。患者术后恢复良好，在术后6个月的MRI随访中未见复发。
脑室内脂肪神经细胞瘤临床病程良好，影像学特征可能有助于术前诊断这种罕见肿瘤。在侧脑室肿瘤的鉴别诊断中应考虑幕上脑室内位置。
