Division of Dermatology, Department of Medical Clinics, Ribeirão Preto Medical School, University of São Paulo, Av. Bandeirantes, 3900, Ribeirao Preto, São Paulo, 14049-900, Brazil.
Division of Clinical Immunology, Department of Medical Clinics, Ribeirão Preto Medical School, University of São Paulo, Ribeirao Preto, Brazil.
Immunol Res. 2018 Oct;66(5):567-576. doi: 10.1007/s12026-018-9028-1.
Bullous pemphigoid (BP) following dementia diagnosis has been reported in the elderly. Skin and brain tissues express BP180 and BP230 isoforms. Dementia has been associated with rs6265 (Val66Met) polymorphism of the brain-derived neurotrophic factor (BDNF) gene and low serum BDNF. Here we investigated a possible cross-antigenicity between BP180/BP230 brain and skin isoforms. We assessed antibodies against BP180/BP230 and BDNF levels by ELISA and BDNF Val66Met SNP by PCR in three groups: 50 BP patients, 50 patients with dementia, and 50 elderly controls. Heatmap hierarchical clustering and data mining decision tree were used to analyze the patients' demographic and laboratorial data as predictors of dementia-BP association. Sixteen percent of BP patients with the lowest serological BDNF presented dementia-BP clinical association. Anti-BP180/230 positivity was unexpected observed among dementia patients (10%, 10%) and controls (14%, 1%). Indirect immunofluorescence using healthy human skin showed a BP pattern in two of 10 samples containing antibodies against BP180/BP230 obtained from dementia group but not in the control samples. Neither allelic nor genotypic BDNF Val66Met SNP was associated with dementia or with BP (associated or not with clinical manifestation of dementia). Heatmap analysis was able to differentiate the three studied groups and confirmed the ELISA results. The comprehensive data mining analysis revealed that BP patients and dementia patients shared biological predictors that justified the dementia-BP association. Autoantibodies against the BP180/BP230 brain isoforms produced by dementia patients could cross-react with the BP180/BP230 skin isoforms, which could justify cases of dementia preceding the BP disease.
大疱性类天疱疮(BP)在老年痴呆症患者中已有报道。皮肤和脑组织表达 BP180 和 BP230 同种型。痴呆症与脑源性神经营养因子(BDNF)基因的 rs6265(Val66Met)多态性和血清 BDNF 水平降低有关。在此,我们研究了 BP180/BP230 脑和皮肤同种型之间可能存在的交叉抗原性。我们通过 ELISA 评估了针对 BP180/BP230 的抗体和 BDNF 水平,并通过 PCR 评估了 BDNF Val66Met SNP,研究了三组患者:50 名 BP 患者,50 名痴呆症患者和 50 名老年对照组。使用热图层次聚类和数据挖掘决策树分析患者的人口统计学和实验室数据,作为痴呆症-BP 关联的预测因子。血清 BDNF 水平最低的 16%BP 患者表现出痴呆症-BP 的临床关联。令人意外的是,在痴呆症患者(10%,10%)和对照组(14%,1%)中也观察到抗 BP180/230 阳性。使用健康人的皮肤进行间接免疫荧光显示,从痴呆症组获得的针对 BP180/BP230 的 10 个样本中的 2 个样本中含有 BP 模式,但对照组样本中没有。BDNF Val66Met SNP 的等位基因或基因型均与痴呆症或与痴呆症无关的 BP 无关。热图分析能够区分这三个研究组,并证实了 ELISA 结果。全面的数据挖掘分析揭示了 BP 患者和痴呆症患者具有共同的生物学预测因子,这证明了痴呆症-BP 之间存在关联。由痴呆症患者产生的针对 BP180/BP230 脑同种型的自身抗体可能与 BP180/BP230 皮肤同种型发生交叉反应,这可以解释在 BP 疾病之前发生痴呆症的情况。