Fabbri Nicolò, Tamburini Nicola, Galeotti Roberto, Quarantotto Francesco, Maniscalco Pio, Rinaldi Rosa, Salviato Elisabetta, Cavallesco Giorgio
Department of Morphology, Experimental Medicine and Surgery, Section of Chirurgia 1, Section of Pathology, Sant'Anna Hospital, University of Ferrara, Ferrara, Italy.
Department of Radiology, Section of Interventional Radiology, Section of Pathology, Sant'Anna Hospital, University of Ferrara, Ferrara, Italy.
AME Case Rep. 2018 May 6;2:19. doi: 10.21037/acr.2018.04.01. eCollection 2018.
Pulmonary sequestration is a congenital malformation characterized by cystic, non-functioning embryonic lung tissue supplied by an abnormal systemic artery. It's a rare disease widely variable in clinical presentation and severity, depending mostly on the degree of lung involvement and location in the thoracic cavity. Most patients have recurrent infections and inflammatory conditions in the affected lobe. Surgical resection continues to be the gold standard of therapy and in this context anatomical resection is the procedure of choice and yields excellent long-term results. There are few studies reporting the use of combined endovascular and thoracoscopic approaches for pulmonary sequestration. We describe a case of intralobar pulmonary sequestration located in the lower lobe of the right lung, which was treated with video-assisted thoracoscopic surgery (VATS) after endovascular embolization of systemic artery arising from celiac trunk.
肺隔离症是一种先天性畸形，其特征为存在由异常体动脉供血的囊性、无功能的胚胎肺组织。这是一种罕见疾病，临床表现和严重程度差异很大，主要取决于肺部受累程度和在胸腔内的位置。大多数患者在受累肺叶会出现反复感染和炎症。手术切除仍然是治疗的金标准，在这种情况下，解剖性切除是首选方法，可产生优异的长期效果。很少有研究报道采用血管内和胸腔镜联合方法治疗肺隔离症。我们描述了一例位于右肺下叶的叶内型肺隔离症病例，该病例在对发自腹腔干的体动脉进行血管内栓塞后，接受了电视辅助胸腔镜手术（VATS）治疗。
