Centre de Recherche du CHU de Québec (CHUQ), Axe Neurosciences, Québec, QC, Canada.
John van Geest Centre for Brain Repair and Department of Clinical Neuroscience, University of Cambridge, Cambridge, United Kingdom.
Ann Neurol. 2018 Dec;84(6):950-956. doi: 10.1002/ana.25354. Epub 2018 Oct 25.
For patients with incurable neurodegenerative disorders such as Huntington's (HD) and Parkinson's disease, cell transplantation has been explored as a potential treatment option. Here, we present the first clinicopathological study of a patient with HD in receipt of cell-suspension striatal allografts who took part in the NEST-UK multicenter clinical transplantation trial. Using various immunohistochemical techniques, we found a discrepancy in the survival of grafted projection neurons with respect to grafted interneurons as well as major ongoing inflammatory and immune responses to the grafted tissue with evidence of mutant huntingtin aggregates within the transplant area. Our results indicate that grafts can survive more than a decade post-transplantation, but show compromised survival with inflammation and mutant protein being observed within the transplant site. Ann Neurol 2018;84:950-956.
对于亨廷顿病(HD)和帕金森病等无法治愈的神经退行性疾病患者,细胞移植已被探索作为一种潜在的治疗选择。在这里,我们报告了首例接受悬浮细胞纹状体同种异体移植物的 HD 患者的临床病理研究,该患者参加了 NEST-UK 多中心临床移植试验。使用各种免疫组织化学技术,我们发现移植的投射神经元的存活与移植的中间神经元之间存在差异,以及对移植组织的持续的炎症和免疫反应,证据表明移植区域内存在突变亨廷顿蛋白聚集体。我们的结果表明,移植物在移植后可以存活 10 年以上,但在移植部位观察到炎症和突变蛋白时,移植物的存活受到影响。神经病学杂志 2018;84:950-956。