Kaplunova V Yu, Shakar'yants G A, Kozhevnikova M V, Khabarova N V, Privalova E V, Belenkov Yu N
Klin Med (Mosk). 2016;94(10):754-63.
This review presents modern data about a hereditary disease of myocardium - hypertrophic cardiomyopathy. The main features of its epidemiology, pathophysiological changes in intracardiac hemodynamics, formation of main clinical symptoms of the disease and variants of its clinical course are considered in terms of modern concepts. Much attention is given to characteristics of the variants of the disease and understanding of the formation of its clinical picture of each of them for the choice of the strategy for the management of these patients.
本综述介绍了关于心肌遗传性疾病——肥厚型心肌病的现代数据。从现代概念的角度考虑了其流行病学的主要特征、心内血流动力学的病理生理变化、该疾病主要临床症状的形成及其临床病程的变体。重点关注了该疾病变体的特征以及对每种变体临床表现形成的理解，以便为这些患者选择管理策略。
