先天性静止性夜盲中的反常瞳孔反应。

Paradoxical pupillary responses in congenital stationary night blindness.

作者信息

Barricks M E, Flynn J T, Kushner B J

出版信息

Arch Ophthalmol. 1977 Oct;95(10):1800-4. doi: 10.1001/archopht.1977.04450100102012.

DOI:10.1001/archopht.1977.04450100102012

Abstract

Three unrelated boys, ages 2, 6, and 10 years, who have congenital stationary night blindness with myopia and a Schubert-Bornschein-type electroretinogram finding, were found to show a "paradoxical" pupillary constriction in darkness. When examining room lights are turned out, the patient's pupils briskly constrict and slowly dilate. Older night blind male relatives of these boys did not show this abnormal constriction to darkness.

摘要

三名年龄分别为2岁、6岁和10岁的无关男孩，患有先天性静止性夜盲伴近视，且视网膜电图检查结果为舒伯特 - 博恩施泰因型，他们在黑暗中出现了“反常”的瞳孔收缩。当检查室的灯熄灭时，患者的瞳孔迅速收缩，然后缓慢扩张。这些男孩的年长夜盲男性亲属在黑暗中未表现出这种异常收缩。