Kweh Barry Ting Sheen, Pham Chengde, McLean Catriona, Tee Jin Wee
Department of Neurosurgery, Level 1, Old Baker Building, The Alfred Hospital, 55 Commercial Rd, Melbourne, Victoria 3004, Australia.
Department of Anatomical Pathology, The Alfred Hospital, 55 Commercial Rd, Melbourne, Victoria 3004, Australia.
J Clin Neurosci. 2018 Oct;56:186-187. doi: 10.1016/j.jocn.2018.06.031. Epub 2018 Jun 30.
Hemangiopericytomas are rare mesenchymal tumors with propensity to recur locally and metastasize. We report the unique case of a fifty-five-year-old male with recurrence of a previously resected craniocervical hemangiopericytoma presenting with obstructive hydrocephalus secondary to new metastatic cerebellar deposits. Emergent surgical resection of the cerebellar hemangiopericytomas was performed prior to adjuvant radiotherapy. Hemangiopericytomas are rare but important differentials for craniocervical junction lesions. Gross total resection remains the cornerstone of management with post-operative radiotherapy and chemotherapy as potential adjuncts. Tumors located in deep regions pose complex management challenges as safe maximal excision may be limited by proximal eloquent structures.
血管外皮细胞瘤是一种罕见的间叶性肿瘤，容易局部复发和转移。我们报告了一例独特的病例，一名55岁男性，之前切除的颅颈血管外皮细胞瘤复发，出现梗阻性脑积水，继发于新的小脑转移性沉积物。在辅助放疗之前，对小脑血管外皮细胞瘤进行了紧急手术切除。血管外皮细胞瘤是颅颈交界区病变中罕见但重要的鉴别诊断。根治性手术切除仍然是治疗的基石，术后放疗和化疗作为潜在辅助手段。位于深部区域的肿瘤带来了复杂的治疗挑战，因为安全的最大切除可能受到近端功能区结构的限制。
